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Items 1 to 97 of about 97
1. Ferreira LM, Emerich PS, Diniz LM, Lage L, Redighieri I: [Langerhans cell histiocytosis: Letterer-Siwe disease - the importance of dermatological diagnosis in two cases]. An Bras Dermatol; 2009 Jul-Aug;84(4):405-9
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  • [Title] [Langerhans cell histiocytosis: Letterer-Siwe disease - the importance of dermatological diagnosis in two cases].
  • [Transliterated title] Histiocitose de células de Langerhans: doença de Letterer-Siwe - importância do diagnóstico dermatológico em dois casos.
  • Langerhans cell histiocytosis is defined as a clonal proliferation of Langerhans phenotypic-like cells.
  • Letterer-Siwe disease is the most common and serious of these entities, affecting mainly infants up to two years of age.
  • We present two cases of this rare disease, diagnosed after dermatological examination, highlighting its typical aspects.
  • [MeSH-major] Histiocytosis, Langerhans-Cell

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  • (PMID = 19851674.001).
  • [ISSN] 1806-4841
  • [Journal-full-title] Anais brasileiros de dermatologia
  • [ISO-abbreviation] An Bras Dermatol
  • [Language] por
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] Brazil
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2. Hammami H, Zaraa I, El Euch D, Chelly I, Haouet S, Mokni M, Ben Osman A: Letterer-Siwe disease associated with chronic myelomyonocytic leukemia: a fortuitous association? Acta Dermatovenerol Alp Pannonica Adriat; 2010;19(1):45-8

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  • [Title] Letterer-Siwe disease associated with chronic myelomyonocytic leukemia: a fortuitous association?
  • Langerhans cell histiocytosis (LCH) and malignancy occurring in the same individual is unusual and has generally been the subject of isolated case reports.
  • Its cause is uncertain but, with the recent demonstration of clonality and its association with malignant disease, there has been a renewal of interest.
  • We report a singular case of Letterer-Siwe disease associated with a chronic myelomonocytic leukemia developing in an elderly woman.
  • The simultaneous occurrence of both malignant disorders supports the hypothesis of a common genetic origin.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / complications. Histiocytosis, Langerhans-Cell / pathology. Leukemia, Myelomonocytic, Chronic / complications

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  • (PMID = 20372775.001).
  • [ISSN] 1581-2979
  • [Journal-full-title] Acta dermatovenerologica Alpina, Pannonica, et Adriatica
  • [ISO-abbreviation] Acta Dermatovenerol Alp Pannonica Adriat
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Slovenia
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3. Salehpour F, Tubbs RS, Zarrintan S, Meshkini A, Hadidchi S, Pourfathi H, Azhough R, Fakhrjou A, Goodrich JT, Khaki AA: Rare C-6 vertebral involvement in a child with histiocytosis X: case report. Folia Neuropathol; 2007;45(2):93-7
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  • [Title] Rare C-6 vertebral involvement in a child with histiocytosis X: case report.
  • The authors present a rare case of C-6 vertebral involvement in a 12-year-old boy with histiocytosis X.
  • Pathological assessment showed infiltration of Langerhans cells accompanied by a mixture of many eosinophils, giant cells, neutrophils and foamy cells.
  • In an extensive review of the literature there are very few cases of cervical histiocytosis X reported.


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4. Negrin-Dastis S, Butenda D, Dorzee J, Fastrez J, d'Odémont JP: Complete disappearance of lung abnormalities on high-resolution computed tomography: a case of histiocytosis X. Can Respir J; 2007 May-Jun;14(4):235-7
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  • [Title] Complete disappearance of lung abnormalities on high-resolution computed tomography: a case of histiocytosis X.
  • A case of pulmonary Langerhans cell histiocytosis, proved by both lung high-resolution computed tomography and lung biopsy, is described.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / radiography. Lung / radiography

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  • (PMID = 17551600.001).
  • [ISSN] 1198-2241
  • [Journal-full-title] Canadian respiratory journal
  • [ISO-abbreviation] Can. Respir. J.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Canada
  • [Other-IDs] NLM/ PMC2676369
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5. Madrigal-Martínez-Pereda C, Guerrero-Rodríguez V, Guisado-Moya B, Meniz-García C: Langerhans cell histiocytosis: literature review and descriptive analysis of oral manifestations. Med Oral Patol Oral Cir Bucal; 2009 May;14(5):E222-8
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  • [Title] Langerhans cell histiocytosis: literature review and descriptive analysis of oral manifestations.
  • Langerhans cell histiocytosis (LCH) is a rare disease, of unknown pathogenesis, characterized by intense and abnormal proliferation of bone marrow-derived histiocytes (Langerhans cells).
  • It can present both local and systemic manifestations involving bone, skin and mucosal tissue, and internal organs.
  • Three basic clinical forms develop: Letterer-Siwe disease (subacute or acute disseminated form), Hand-Schüller-Christian disease (disseminated chronic form) and eosinophilic granuloma (localized chronic form).
  • The principal differential diagnoses include advanced periodontal disease or a periapical process of dental or periodontal origin.
  • The odontologist plays a vital role in the diagnosis and multidisciplinary treatment of such patients, by performing routine examinations for periodic follow-up of the disease and its possible oral manifestations, bearing in mind that these may be the first or only signs of LCH.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / complications. Mouth Diseases / etiology

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  • (PMID = 19218906.001).
  • [ISSN] 1698-6946
  • [Journal-full-title] Medicina oral, patología oral y cirugía bucal
  • [ISO-abbreviation] Med Oral Patol Oral Cir Bucal
  • [Language] eng
  • [Publication-type] Journal Article; Review
  • [Publication-country] Spain
  • [Number-of-references] 28
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6. Lee CG, Lim YJ, Choi JS, Lee JH: Filiform polyposis in the sigmoid colon: a case series. World J Gastroenterol; 2010 May 21;16(19):2443-7
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  • Filiform polyposis is a rare condition of uncertain pathogenesis that is usually found in association with Crohn's disease, ulcerative colitis, intestinal tuberculosis or histiocytosis X.
  • We report seven interesting cases of polyposis with various pathologic components, mainly located in the left side of the colon with no associated inflammatory bowel disease, intestinal tuberculosis or histiocytosis X.

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  • (PMID = 20480534.001).
  • [ISSN] 2219-2840
  • [Journal-full-title] World journal of gastroenterology
  • [ISO-abbreviation] World J. Gastroenterol.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] China
  • [Other-IDs] NLM/ PMC2874153
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7. Dina I, Copaescu C, Herlea V, Wrba F, Iacobescu C: Liver involvement in Langerhans' cell histiocytosis. Case report. J Gastrointestin Liver Dis; 2006 Mar;15(1):57-9
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  • [Title] Liver involvement in Langerhans' cell histiocytosis. Case report.
  • Langerhans'cell histiocytosis (Histiocytosis X) is a rare disease of unknown cause characterized by oligoclonal proliferation of Langerhans cells.
  • The diagnosis is always made by a histological approach.
  • We report a case of Langerhans'cell histiocytosis in a young patient with clinical signs of diabetes insipidus and hepatic involvement in whom the immunohistochemical analysis of the liver tissue led to the definitive diagnosis.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / pathology. Liver Diseases / etiology. Liver Diseases / pathology

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  • (PMID = 16680234.001).
  • [ISSN] 1841-8724
  • [Journal-full-title] Journal of gastrointestinal and liver diseases : JGLD
  • [ISO-abbreviation] J Gastrointestin Liver Dis
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Romania
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8. Pant C, Madonia P, Bahna SL, Bass PF, Jeroudi M: Langerhans cell histiocytosis, a case of Letterer Siwe disease. J La State Med Soc; 2009 Jul-Aug;161(4):211-2
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  • [Title] Langerhans cell histiocytosis, a case of Letterer Siwe disease.
  • An 8-month-old male infant presented with a progressively worsening generalized rash of 5-6 months duration, fever, poor feeding, and abdominal distension.
  • The patient was started on i.v. antibiotics, and a working diagnosis of Langerhans cell histiocytosis was reached that was later confirmed with a skin biopsy.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / diagnosis. Histiocytosis, Langerhans-Cell / drug therapy

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  • (PMID = 19785312.001).
  • [ISSN] 0024-6921
  • [Journal-full-title] The Journal of the Louisiana State Medical Society : official organ of the Louisiana State Medical Society
  • [ISO-abbreviation] J La State Med Soc
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] United States
  • [Chemical-registry-number] 0 / Antineoplastic Agents; 04079A1RDZ / Cytarabine; 47M74X9YT5 / Cladribine; 5V9KLZ54CY / Vinblastine; VB0R961HZT / Prednisone
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9. Iupati D, Chander S: A case report of langerhans histiocytosis presenting sequentially over a 21-year period with Letterer-Siwe disease, hand-Schuller-Christian disease and eosinophillic granuloma of bone. J Pediatr Hematol Oncol; 2006 Nov;28(11):746-9
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  • [Title] A case report of langerhans histiocytosis presenting sequentially over a 21-year period with Letterer-Siwe disease, hand-Schuller-Christian disease and eosinophillic granuloma of bone.
  • Langerhans cell histiocytosis (LCH) is a very rare disorder, and usually considered a disease of childhood.
  • The adult form of LCH is even rare, and in some case may be considered to represent delayed presentation of a pathologic process beginning in childhood.
  • [MeSH-major] Eosinophilic Granuloma / complications. Histiocytosis, Langerhans-Cell / complications. Histiocytosis, Langerhans-Cell / diagnosis. Xanthomatosis / complications

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  • (PMID = 17114962.001).
  • [ISSN] 1077-4114
  • [Journal-full-title] Journal of pediatric hematology/oncology
  • [ISO-abbreviation] J. Pediatr. Hematol. Oncol.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] United States
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10. Pérez-Martínez J, Marques M, Kilmurray L, Medina I, Nam-Cha SH, Llamas F, Gómez C, Barrientos A, Blanco J: Secondary amyloidosis associated with histiocytosis X. Amyloid; 2008 Mar;15(1):69-71
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  • [Title] Secondary amyloidosis associated with histiocytosis X.
  • We report a 34-year-old man diagnosed with Langerhans cell histiocytosis (LCH) or histiocytosis X in 1980.
  • He had multiple focal osseous lesions, difficult control of the disease activity and was treated many times with chemo- and radiotherapy for symptomatic control.
  • His kidney disease started 20 years after the diagnosis with progressive renal failure and increasing non-nephrotic proteinuria, coinciding with two flares of LCH.
  • [MeSH-major] Amyloidosis / diagnosis. Amyloidosis / etiology. Histiocytosis, Langerhans-Cell / complications
  • [MeSH-minor] Adult. Biopsy. Humans. Male. Proteinuria / complications. Proteinuria / diagnosis. Proteinuria / pathology. Proteinuria / therapy. Renal Insufficiency / complications. Renal Insufficiency / diagnosis. Renal Insufficiency / pathology. Renal Insufficiency / therapy

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  • (PMID = 18266125.001).
  • [ISSN] 1350-6129
  • [Journal-full-title] Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis
  • [ISO-abbreviation] Amyloid
  • [Language] eng
  • [Publication-type] Letter
  • [Publication-country] United States
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11. Skoulakis CE, Drivas EI, Papadakis CE, Bizaki AJ, Stavroulaki P, Helidonis ES: Langerhans cell histiocytosis presented as bilateral otitis media and mastoiditis. Turk J Pediatr; 2008 Jan-Feb;50(1):70-3
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  • [Title] Langerhans cell histiocytosis presented as bilateral otitis media and mastoiditis.
  • Langerhans cell histiocytosis (LCH) is a rare disease that may affect multiple organs.
  • It is currently believed that clonal accumulation and proliferation of CD1a-positive Langerhans cells are causative.
  • The term LCH or histiocytosis X refers to three separate illnesses (listed in order of increasing severity): eosinophilic granuloma, Hand-Schüller-Christian disease and Letterer-Siwe disease.
  • The signs and symptoms of otologic histiocytosis can mimic those of acute and chronic infectious ear disease.
  • Only a surgically obtained biopsy leads to definitive diagnosis and appropriate therapy.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / diagnosis. Mastoiditis / diagnosis
  • [MeSH-minor] Diagnosis, Differential. Fatal Outcome. Humans. Infant. Male. Rare Diseases. Tomography, X-Ray Computed

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  • (PMID = 18365596.001).
  • [ISSN] 0041-4301
  • [Journal-full-title] The Turkish journal of pediatrics
  • [ISO-abbreviation] Turk. J. Pediatr.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Turkey
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12. Jalil Ab, Hin-Lau S: Oral Langerhans cell histiocytosis in Malaysian children: a 40-year experience. Int J Paediatr Dent; 2009 Sep;19(5):349-53
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  • [Title] Oral Langerhans cell histiocytosis in Malaysian children: a 40-year experience.
  • BACKGROUND: Oral Langerhans cell histiocytosis is generally seen in children.
  • METHODS: A retrospective study was carried out to determine the clinicopathological features of Langerhans cell histiocytosis (LCH), Letterer-Siwe disease, Hand-Schuller-Christian disease, eosinophilic granuloma, and histiocytosis X occurring in the oral cavity in children, diagnosed histologically in the main oral histopathology laboratory in Malaysia from 1967 to 2007.
  • The patients also had other systemic signs and symptoms: skin lesions (n = 5), hepatosplenomegaly (n = 2), prolonged fever (n = 2), diabetes insipidus (n = 1), and exophthalmos (n = 1).
  • Two cases were known cases of systemic LCH.
  • CONCLUSION: The histopathologic features of LCH are easily recognized; however, with the development of immunostaining, the use of CD1a helps in confirming the diagnosis.

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  • (PMID = 19486369.001).
  • [ISSN] 1365-263X
  • [Journal-full-title] International journal of paediatric dentistry
  • [ISO-abbreviation] Int J Paediatr Dent
  • [Language] ENG
  • [Publication-type] Journal Article
  • [Publication-country] England
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13. Jain S, Kanarek N, Arceci RJ: Analysis of histiocytosis deaths in the US and recommendations for incidence tracking. J Registry Manag; 2010;37(4):156-62
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  • [Title] Analysis of histiocytosis deaths in the US and recommendations for incidence tracking.
  • OBJECTIVE: We determined the frequency of deaths associated with histiocytosis in the United States (US) for which incidence data are lacking and could be potentially important in understanding outcomes for patients with these disorders.
  • METHODS: National death data collected by the US Vital Statistics Reporting System and aggregated using wonder.cdc.gov were analyzed for underlying cause of death due to malignant histiocytosis (MH), Langerhans cell histiocytosis (LCH) and Letterer-Siwe disease (LS, a form of LCH) for 3 periods: 1979-1988, 1989-1998, and 1999-2006.
  • To capture histiocytosis, International Classification of Diseases (ICD)-9 codes 202.3, 202.5, and 277.8 and ICD-10 codes C96.1, C96.0, and D76.0-76.1 were used.
  • Other listed contributing causes of death with a histiocytosis diagnosis were also examined.
  • RESULTS: A total of 2,416 deaths primarily due to histiocytosis as underlying cause occurred between 1979 and 2006.
  • On comparison of the underlying and contributory cause for the period 1999-2006, histiocytosis mentioned on the death certificate as a contributory cause (N=562) occurs nearly as often as does underlying cause alone (N=648).
  • The age-adjusted (year 2000) death rate was highest for MH (2.62 deaths per 10 million, 95% CI: 2.40-2.83) and for LCH and LS disease (2.17, 95% CI: 1.98-2.36) during the period 1979-1988.
  • Death rates of each type of histiocytosis dropped significantly from 1979 to 1988 to 1999-2006 (p-value <0.0001).
  • CONCLUSIONS/DISCUSSION: Death due to histiocytosis or histiocytosis-related causes is a rare event that is trackable in the US by person, place and time characteristics.
  • However, a population-based, disease incidence registry has begun to accurately ascertain incidence cases, which will facilitate study of these conditions.
  • [MeSH-major] Histiocytosis / mortality. Registries

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  • (PMID = 21688746.001).
  • [ISSN] 1945-6123
  • [Journal-full-title] Journal of registry management
  • [ISO-abbreviation] J Registry Manag
  • [Language] eng
  • [Publication-type] Journal Article; Research Support, Non-U.S. Gov't
  • [Publication-country] United States
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14. Pavlović MD, Minić A, Zolotarevski L, Vesić S: Disseminated crusted papules in a newborn. Vojnosanit Pregl; 2006 Jul;63(7):681-3
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  • [Title] Disseminated crusted papules in a newborn.
  • BACKGROUND: Congenital self-healing Langerhans cell histiocytosis (Hashimoto-Pritzker disease) is the rarest form of Langerhans cell histiocytosis, usually confined to the skin and/or mucous membranes.
  • Cutaneous eruption is mostly generalized, papular, nodular or vesicular.
  • Despite impressive clinical presentation in a newborn it infrequently spreads to internal organs (which then portends a grave prognosis, indistinguishable from Letterer-Siwe disease).
  • CONCLUSION: There is no need for specific treatment of congenital self-healing Langerhans cell-histiocytosis in the absence of multiorgan involvement.
  • However, a close and regular follow-up is necessary to evaluate the children for systemic symptoms and signs.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / congenital. Histiocytosis, Langerhans-Cell / pathology. Skin Diseases / congenital. Skin Diseases / pathology

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  • (PMID = 16875431.001).
  • [ISSN] 0042-8450
  • [Journal-full-title] Vojnosanitetski pregled
  • [ISO-abbreviation] Vojnosanit Pregl
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Serbia and Montenegro
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15. Zhou HM, Zeng X, Chen QM: [Clinical and pathologic features of Letterer-Siwe disease: a case report and review]. Hua Xi Kou Qiang Yi Xue Za Zhi; 2007 Oct;25(5):517-9

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  • [Title] [Clinical and pathologic features of Letterer-Siwe disease: a case report and review].
  • Letterer-Siwe disease (LSD) is a kind of a histiocytosis, rarely seen in clinic.
  • A case of LSD which complaints of the oral ulcer is reported in this article.
  • No familial history of genetic diseases and special infections were found.
  • The pathologic exam showed histioid cell infiltration, and the immunohistochemical exam showed CDla(+), S-100(+).
  • Diagnosis defined it LSD.
  • According to the case's character and literature review, the clinical features, diagnosis and therapy of LSD were discussed.
  • [MeSH-major] Histiocytosis, Langerhans-Cell. Skin

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  • (PMID = 18072575.001).
  • [ISSN] 1000-1182
  • [Journal-full-title] Hua xi kou qiang yi xue za zhi = Huaxi kouqiang yixue zazhi = West China journal of stomatology
  • [ISO-abbreviation] Hua Xi Kou Qiang Yi Xue Za Zhi
  • [Language] chi
  • [Publication-type] Case Reports; English Abstract; Journal Article; Review
  • [Publication-country] China
  • [Chemical-registry-number] Familial Letterer-Siwe disease
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16. Ben Slama L, Ruhin B, Zoghbani A: [Langerhans cell histiocytosis]. Rev Stomatol Chir Maxillofac; 2009 Nov;110(5):287-9
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  • [Title] [Langerhans cell histiocytosis].
  • [Transliterated title] Histiocytose langerhansienne.
  • Langerhans cell histiocytosis (ex histiocytosis X) is usually present in children.
  • It is a clonal proliferation of non-functional Langerhans's cells.
  • The diagnosis is made in immunolabeling by anti-CD1a.
  • Clinical presentations are variable, depending on their extension.
  • Three syndromes are actually the same pathogenic process: eosinophilic granuloma (single or multiple osseous localizations), Hand-Schüller-Christian disease (chronic form with bone and visceral dissemination) and Abt-Letterer-Siwe disease (disseminated and acute malignant presentation).
  • [MeSH-major] Histiocytosis, Langerhans-Cell / classification. Histiocytosis, Langerhans-Cell / pathology

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  • (PMID = 19828161.001).
  • [ISSN] 1776-257X
  • [Journal-full-title] Revue de stomatologie et de chirurgie maxillo-faciale
  • [ISO-abbreviation] Rev Stomatol Chir Maxillofac
  • [Language] fre
  • [Publication-type] English Abstract; Journal Article; Review
  • [Publication-country] France
  • [Number-of-references] 11
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17. Alloh Amichia YC, Le Bars P, Giumelli B, Soueidan A: [Prosthetic rehabilitation after osteonecrosis of the jaws due to histiocytosis X and treatment with bisphosphonates apropos of a case]. Odontostomatol Trop; 2010 Dec;33(132):34-40
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  • [Title] [Prosthetic rehabilitation after osteonecrosis of the jaws due to histiocytosis X and treatment with bisphosphonates apropos of a case].
  • [Transliterated title] Réhabilitation prothétique après ostéonécrose des maxillaires due à une histiocytose X et un traitement aux bisphosphonates à propos d'un cas.
  • In this article, we present the clinical case of a patient with histiocytois treated by bisphosphonates and having developed ONJ.
  • [MeSH-major] Bone Density Conservation Agents / adverse effects. Diphosphonates / adverse effects. Histiocytosis, Langerhans-Cell / drug therapy. Jaw, Edentulous, Partially / rehabilitation. Mandibular Diseases / chemically induced. Osteonecrosis / chemically induced

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  • (PMID = 21510356.001).
  • [ISSN] 0251-172X
  • [Journal-full-title] Odonto-stomatologie tropicale = Tropical dental journal
  • [ISO-abbreviation] Odontostomatol Trop
  • [Language] fre
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] Senegal
  • [Chemical-registry-number] 0 / Bone Density Conservation Agents; 0 / Diphosphonates; 0 / Imidazoles; 6XC1PAD3KF / zoledronic acid; OYY3447OMC / pamidronate; X1J18R4W8P / Alendronate
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18. Lahiani D, Hammami BK, Maâloul I, Frikha M, Baklouti S, Jlidi R, Ben Jemaâ M: [Multifocal Langerhans cell histiocytosis of bone: late revelation in a 76-year-old woman]. Rev Med Interne; 2008 Mar;29(3):249-51
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  • [Title] [Multifocal Langerhans cell histiocytosis of bone: late revelation in a 76-year-old woman].
  • [Transliterated title] Histiocytose langerhansienne osseuse multifocale: révélation tardive chez une femme de 76 ans.
  • Langerhans cell histiocytosis or histiocytosis X has a variable course from a self-limited eosinophilic granuloma to an aggressive disseminated disease.
  • We report a 76-year-old woman with multifocal bone histiocytosis X, involving the rachis, an iliac bone and the skull.
  • The diagnosis has been established by histological exam.

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  • (PMID = 18242789.001).
  • [ISSN] 0248-8663
  • [Journal-full-title] La Revue de medecine interne
  • [ISO-abbreviation] Rev Med Interne
  • [Language] FRE
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] France
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19. Saleem I, Moss J, Egan JJ: Lung transplantation for rare pulmonary diseases. Sarcoidosis Vasc Diffuse Lung Dis; 2005 Dec;22 Suppl 1:S85-90
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  • This article will present an overview of lung transplantation in the context of rare pulmonary diseases, in particular pulmonary sarcoidosis, lymphangioleiomyomatosis (LAM), and pulmonary Langerhans Cell Histiocytosis X (LCH).

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  • (PMID = 16457020.001).
  • [ISSN] 1124-0490
  • [Journal-full-title] Sarcoidosis, vasculitis, and diffuse lung diseases : official journal of WASOG
  • [ISO-abbreviation] Sarcoidosis Vasc Diffuse Lung Dis
  • [Language] ENG
  • [Publication-type] Comparative Study; Journal Article; Review
  • [Publication-country] Italy
  • [Number-of-references] 20
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20. Zeppa P, Cozzolino I, Russo M, Cataldo PT, Vetrani A, Palombini L: Pulmonary langerhans cell histiocytosis (histiocytosis X) on bronchoalveolar lavage: a report of 2 cases. Acta Cytol; 2007 May-Jun;51(3):480-2
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  • [Title] Pulmonary langerhans cell histiocytosis (histiocytosis X) on bronchoalveolar lavage: a report of 2 cases.
  • BACKGROUND: Pulmonary Langerhans cell histiocytosis (PLCH) is an interstitial lung disease characterized by bilateral nodular and cystic lesions.
  • CASES: In 2 cases of PLCH, cytologic and immunocytochemical evaluation of bronchoalveolar lavage (BAL) fluid was successfully used for the diagnosis of PLCH.
  • Cytospins showed a monomorphous and dispersed cell population consisting ofmononucleated or binucleated and occasionally multinucleated histiocytes.
  • In both cases the cytologic diagnosis of PLCH was confirmed by subsequent CT and clinical follow-up.
  • CONCLUSION: Cytologic and immunocytochemical evaluation of BAL fluid permits a definitive diagnosis of PLCH.
  • This cytologic diagnosis is clinically relevant because it permits surgical biopsy to be bypassed and allows waiting for a possible spontaneous or pharmacologic resolution.
  • [MeSH-major] Bronchoalveolar Lavage Fluid / cytology. Histiocytosis, Langerhans-Cell / pathology. Langerhans Cells / pathology

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  • (PMID = 17536561.001).
  • [ISSN] 0001-5547
  • [Journal-full-title] Acta cytologica
  • [ISO-abbreviation] Acta Cytol.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] United States
  • [Chemical-registry-number] 0 / Antigens, CD1; 0 / CD1a antigen
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21. Asensio-Sánchez VM, Calvo-Crespo MJ: [Orbital involvement as the first manifestation of Hand-Schuller-Christian disease. A case report]. Arch Soc Esp Oftalmol; 2005 Aug;80(8):483-5
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Orbital involvement as the first manifestation of Hand-Schuller-Christian disease. A case report].
  • [Transliterated title] AFectación orbitaria como primera manifestación de la enfermedad de Hand-Schuller-Christian. Caso clínico.
  • PURPOSE/MATERIAL AND METHOD: To describe the clinical case of a 20-month-old boy with Hand-Schuller-Christian disease.
  • Exophthalmos was the only systemic manifestation evident over a period of at least 6 weeks, but later the triad of exophthalmos with multiple lytic lesions of the skull and diabetes insipidus were present.
  • RESULTS/CONCLUSION: Histiocytosis X should be considered in the differential diagnosis of orbital tumors in children.
  • [MeSH-major] Exophthalmos / etiology. Histiocytosis, Langerhans-Cell / diagnosis
  • [MeSH-minor] Age Factors. Diagnosis, Differential. Humans. Infant. Magnetic Resonance Imaging. Male. Time Factors

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  • (PMID = 16136404.001).
  • [ISSN] 0365-6691
  • [Journal-full-title] Archivos de la Sociedad Española de Oftalmología
  • [ISO-abbreviation] Arch Soc Esp Oftalmol
  • [Language] spa
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] Spain
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22. Gérard R, Keller A, Taylor S, Hoffmeyer P, Peter R: [Ischemic eosinophilic granuloma and pulmonary histiocytosis with a regressive course]. Rev Chir Orthop Reparatrice Appar Mot; 2007 Sep;93(5):501-5
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Ischemic eosinophilic granuloma and pulmonary histiocytosis with a regressive course].
  • [Transliterated title] Granulome éosinophile ischiatique et histiocytose pulmonaire d'évolution régressive.
  • Langerhans' histiocytosis or histiocytosis X is a rare intrinsically benign disease producing a destructive tumor with a variable clinical presentation and an often unpredictable clinical course.
  • The lung disease led to the initial diagnosis and optimal surgical, pathological and radiological management.
  • [MeSH-major] Eosinophilic Granuloma. Histiocytosis, Langerhans-Cell
  • [MeSH-minor] Adolescent. Bone Transplantation. Humans. Ischium / radiography. Ischium / surgery. Magnetic Resonance Imaging. Male. Osteolysis / diagnosis. Osteolysis / etiology. Osteotomy. Pelvic Bones / radiography. Radiography, Abdominal. Radiography, Thoracic. Tomography, X-Ray Computed. Treatment Outcome

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  • (PMID = 17878842.001).
  • [ISSN] 0035-1040
  • [Journal-full-title] Revue de chirurgie orthopédique et réparatrice de l'appareil moteur
  • [ISO-abbreviation] Rev Chir Orthop Reparatrice Appar Mot
  • [Language] fre
  • [Publication-type] Case Reports; Comparative Study; English Abstract; Journal Article
  • [Publication-country] France
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23. Portale G, Costantini M, Zaninotto G, Ruol A, Guirroli E, Rampado S, Ancona E: Pseudoachalasia: not only esophago-gastric cancer. Dis Esophagus; 2007;20(2):168-72

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  • Pseudoachalasia is a rare clinical entity which has clinical, radiographic and manometric features often indistinguishable from achalasia.
  • We present three cases of pseudoachalasia in which the primary cause of the disease was not an esophagogastric cancer.
  • The causes were a pancreatic carcinoma, a breast cancer and an histiocytosis X.

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  • (PMID = 17439602.001).
  • [ISSN] 1120-8694
  • [Journal-full-title] Diseases of the esophagus : official journal of the International Society for Diseases of the Esophagus
  • [ISO-abbreviation] Dis. Esophagus
  • [Language] ENG
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] United States
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24. Thelen A, Weikert S, Schrom T, Sedlmaier B: [Histiocytosis of Langerhans cells. Simultaneous manifestation in both mastoid cavities]. HNO; 2009 Oct;57(10):1029-32
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  • [Title] [Histiocytosis of Langerhans cells. Simultaneous manifestation in both mastoid cavities].
  • [Transliterated title] Langerhans-Zell-Histiozytose. Simultane Manifestation in beiden Mastoidhöhlen.
  • Histiocytosis X (Langerhans cells) is a rare disease with different forms of manifestation in the head and neck, which mostly occurs in children.
  • We report the case of a 52-year-old male patient from Saudi Arabia who presented in the out-patient department of the University Hospital Charité Berlin with therapy-resistant otitis externa.
  • Histological evaluation of the suspected tissue revealed histiocytosis X in both mastoids.
  • After exclusion of a systemic disease local low-dose radiotherapy with 9 Gy (3x3 Gy) of the mastoid cavities was administered.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / diagnosis. Histiocytosis, Langerhans-Cell / radiotherapy. Mastoid. Mastoiditis / diagnosis. Mastoiditis / radiotherapy

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  • [Cites] Laryngorhinootologie. 2003 Mar;82(3):166-70 [12673514.001]
  • [Cites] J Laryngol Otol. 2001 Oct;115(10 ):839-41 [11668004.001]
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  • (PMID = 19384539.001).
  • [ISSN] 1433-0458
  • [Journal-full-title] HNO
  • [ISO-abbreviation] HNO
  • [Language] ger
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] Germany
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25. Per H, Koç KR, Gümüş H, Canpolat M, Kumandaş S: Cervical eosinophilic granuloma and torticollis: a case report and review of the literature. J Emerg Med; 2008 Nov;35(4):389-92
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  • EG, a variant of histiocytosis X, is a rare disease causing destructive bony lesions of the cervical spine in children.
  • This report describes the case of a 5-year-old boy with torticollis who presented to the Emergency Department and was found to have EG of C6.
  • [MeSH-major] Cervical Vertebrae / pathology. Eosinophilic Granuloma / diagnosis. Torticollis / diagnosis
  • [MeSH-minor] Child, Preschool. Diagnosis, Differential. Humans. Male. Spinal Fusion / methods

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  • (PMID = 18353598.001).
  • [ISSN] 0736-4679
  • [Journal-full-title] The Journal of emergency medicine
  • [ISO-abbreviation] J Emerg Med
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article; Review
  • [Publication-country] United States
  • [Number-of-references] 23
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26. Sato TS, Ferguson PJ, Khanna G: Primary multifocal osseous lymphoma in a child. Pediatr Radiol; 2008 Dec;38(12):1338-41
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  • We report a case of primary multifocal osseous lymphoma in a 6-year-old girl presenting with multifocal osteolytic lesions without systemic symptoms or identifiable non-osseous primary tumor.
  • The differential diagnoses for such a presentation include histiocytosis X, chronic recurrent multifocal osteomyelitis, acute lymphoblastic leukemia, metastatic disease, and primary bone lymphoma.
  • Although non-Hodgkin lymphoma is common in the pediatric population, its presentation as a primary bone tumor, especially with multifocal disease, is extremely rare and is frequently misdiagnosed.
  • We hope that awareness of this entity will help radiologists achieve timely diagnosis and intervention.
  • [MeSH-major] Bone Neoplasms / diagnosis. Lymphoma, Non-Hodgkin / diagnosis
  • [MeSH-minor] Arthralgia / etiology. Biopsy / methods. Child. Diagnosis, Differential. Female. Femur / pathology. Femur / radiography. Fluorodeoxyglucose F18. Humans. Magnetic Resonance Imaging. Positron-Emission Tomography / methods. Radiopharmaceuticals. Rare Diseases. Tomography, X-Ray Computed. Whole Body Imaging / methods

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  • (PMID = 18779959.001).
  • [ISSN] 0301-0449
  • [Journal-full-title] Pediatric radiology
  • [ISO-abbreviation] Pediatr Radiol
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Germany
  • [Chemical-registry-number] 0 / Radiopharmaceuticals; 0Z5B2CJX4D / Fluorodeoxyglucose F18
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27. Kaul R, Gupta N, Gupta S, Gupta M: Eosinophilic granuloma of skull bone. J Cytol; 2009 Oct;26(4):156-7

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • Eosinophilic granuloma is a variety of histiocytosis-X with unknown etiology.
  • Other sites like the lung and the gastrointestinal tract may also be affected.
  • The radiographic and cytological findings were characteristic of the disease.

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  • [Cites] Cancer. 1999 May 15;85(10):2278-90 [10326709.001]
  • [Cites] Pediatr Radiol. 2005 Feb;35(2):103-15 [15289942.001]
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  • (PMID = 21938183.001).
  • [ISSN] 0974-5165
  • [Journal-full-title] Journal of cytology
  • [ISO-abbreviation] J Cytol
  • [Language] ENG
  • [Publication-type] Journal Article
  • [Publication-country] India
  • [Other-IDs] NLM/ PMC3168004
  • [Keywords] NOTNLM ; Aspiration cytology / eosinophilic granuloma / headache
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28. Chkoura A, El Alloussi M, Taleb B, El Wady W: Resolution of eosinophilic granuloma after minimal intervention. Case report and review of literature. N Y State Dent J; 2010 Mar;76(2):43-6
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  • Langerhans cell histiocytosis (LCH), previously known as histiocytosis X, is a rare, proliferative disorder in which the accumulation of pathologic Langerhans cells leads to local tissue infiltration and destruction.
  • The role of the dentist is important in early and accurate evaluation, staging and diagnosis of LCH, because it may mimic more common diseases, such as juvenile periodontitis and osteomyelitis.
  • The history, radiological appearance, differential diagnosis, histopathology and treatment options for the patient are discussed.
  • [MeSH-minor] Aggressive Periodontitis / diagnosis. Alveolar Bone Loss / surgery. Child. Diagnosis, Differential. Female. Humans. Minimally Invasive Surgical Procedures. Papillon-Lefevre Disease / diagnosis. Tooth Extraction

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  • (PMID = 20441047.001).
  • [ISSN] 0028-7571
  • [Journal-full-title] The New York state dental journal
  • [ISO-abbreviation] N Y State Dent J
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article; Review
  • [Publication-country] United States
  • [Number-of-references] 27
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29. Philippe B, Dromer C, Mornex JF, Velly JF, Stern M: [When should respiratory physicians consider lung transplantation for their patients? Inscription criteria for the national waiting list]. Rev Mal Respir; 2009 Apr;26(4):423-35; quiz 480, 483
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  • [Transliterated title] Quand le pneumologue doit-il envisager la greffe pulmonaire pour un de ses patients?
  • INTRODUCTION: Placing a patient on the national lung transplant waiting list remains a difficult matter, and is more a question of timing than selection of the candidate according to disease-specific criteria.
  • Sarcoidosis, lymphangioleiomyomatosis, histiocytosis X and connective tissue diseases are rare indications for which the listing criteria are similar to those for the more usual respiratory diseases.
  • CONCLUSION: The optimal time for placing lung transplantation patients who have been referred early in the course of their disease on the waiting list will be determined by clinical experience and individual patient follow-up.

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  • (PMID = 19421095.001).
  • [ISSN] 0761-8425
  • [Journal-full-title] Revue des maladies respiratoires
  • [ISO-abbreviation] Rev Mal Respir
  • [Language] fre
  • [Publication-type] English Abstract; Journal Article
  • [Publication-country] France
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30. Niksarlioglu YO, Gurel B, Tezel GG, Firat P, Dogan R, Kars A, Coplu L: Langerhans' cell histiocytosis mimicking metastatic carcinoma of the lung. Respirology; 2009 Apr;14(3):456-8
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  • [Title] Langerhans' cell histiocytosis mimicking metastatic carcinoma of the lung.
  • Langerhans' cell histiocytosis (LCH), previously known as Histiocytosis X, is characterized by abnormal accumulations of large mononuclear cells forming granulomas in various organs, mainly bone, skin and lung.
  • This case report describes a 50-year-old man with a history of left pneumonectomy due to squamous cell carcinoma (SCC).
  • On diagnosis, the patient stopped smoking and was treated with vinblastine and prednisolone for LCH.
  • [MeSH-major] Carcinoma, Squamous Cell / diagnosis. Histiocytosis, Langerhans-Cell / diagnosis. Lung Neoplasms / diagnosis. Neoplasm Recurrence, Local / diagnosis
  • [MeSH-minor] Diagnosis, Differential. Humans. Lung / pathology. Lung / radiography. Male. Middle Aged. Smoking. Tomography, X-Ray Computed


31. Adib AF, Lazrak A, Boulaich M, Nazih N, Oujilal A, Kzadri M: [Mastoid eosinophilic granuloma: a case report]. Rev Laryngol Otol Rhinol (Bord); 2005;126(1):37-41
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Transliterated title] Le granulome éosinophile de la mastoïde: à propos d'un cas.
  • OBJECTIVES: Langerhans cell histiocytosis is a proliferating cell disease that may take various forms characterised by bone, skin lymph nodes and visceral lesions.
  • Eosinophilic granuloma is a localised form of histiocytosis X, or Langerhans' cells histiocytosis, a benign form with unknown aetiology.
  • At the head and neck level, it is usually located on the temporal, and usually occur in association with multifocal disease; however, isolated lesions may occur in the mastoid bone alone.
  • METHODS: The author's present a case of a patient with unifocal eosinophilic granuloma limited to the mastoid treated in ENT and radiotherapy departments.
  • The biopsy and immunohistochemical study confirmed the diagnosis.
  • CONCLUSION: Unifocal eosinophilic granuloma of the temporal bone is a benign lesion of langerhans' cell histiocytosis.
  • Its diagnosis is difficult when the disease remains isolated.
  • [MeSH-major] Bone Diseases / diagnosis. Eosinophilic Granuloma / diagnosis. Mastoid / pathology
  • [MeSH-minor] Adolescent. Biopsy. Female. Follow-Up Studies. Humans. Immunohistochemistry. Osteolysis / diagnosis. Temporal Bone / pathology. Tomography, X-Ray Computed

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  • (PMID = 16080647.001).
  • [ISSN] 0035-1334
  • [Journal-full-title] Revue de laryngologie - otologie - rhinologie
  • [ISO-abbreviation] Rev Laryngol Otol Rhinol (Bord)
  • [Language] fre
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] France
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32. Dhouib H, Hammami B, Sellami M, Mnif L, Boudawara T, Ghorbel A: [Xanthogranuloma of the parotid gland in adults]. Rev Stomatol Chir Maxillofac; 2010 Nov-Dec;111(5-6):337-9
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Transliterated title] Xanthogranulome parotidien de l'adulte.
  • Juvenile xanthogranuloma (JXG) is a cutaneous non-Langerhans cell histiocytosis affecting infants.
  • CLINICAL CASE: A 52 year-old man consulted for a painful swelling of the left parotid region, progressively increasing.
  • In fact, the morphological, immunohistochemical, and ultrastructural features of this affection lead to its diagnosis.
  • The differential diagnosis is X histiocytosis.
  • [MeSH-major] Parotid Diseases / diagnosis. Xanthogranuloma, Juvenile / diagnosis
  • [MeSH-minor] Antigens, CD / analysis. Antigens, Differentiation, Myelomonocytic / analysis. Contrast Media. Diagnosis, Differential. Gadolinium. Humans. Image Enhancement. Macrophages / pathology. Magnetic Resonance Imaging. Male. Middle Aged. Vimentin / analysis

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  • [Copyright] Copyright © 2010. Published by Elsevier Masson SAS.
  • (PMID = 20817224.001).
  • [ISSN] 1776-257X
  • [Journal-full-title] Revue de stomatologie et de chirurgie maxillo-faciale
  • [ISO-abbreviation] Rev Stomatol Chir Maxillofac
  • [Language] fre
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] France
  • [Chemical-registry-number] 0 / Antigens, CD; 0 / Antigens, Differentiation, Myelomonocytic; 0 / CD68 antigen, human; 0 / Contrast Media; 0 / Vimentin; AU0V1LM3JT / Gadolinium
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33. Baltacioğlu E, Senel FC, Ozen B, Ofluoğlu AD, Ersöz S, Kebudi R, Tanyeri H: Clinical, pathological and radiological evaluation of disseminated Langerhans' cell histiocytosis in a 30-month-old boy. Dentomaxillofac Radiol; 2007 Dec;36(8):526-9
Genetic Alliance. consumer health - Langerhans cell histiocytosis.

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  • [Title] Clinical, pathological and radiological evaluation of disseminated Langerhans' cell histiocytosis in a 30-month-old boy.
  • Langerhans' cell histiocytosis is a rare disease characterized histologically by the proliferation of Langerhans' cells.
  • Oral involvement is frequent and the disease simulates severe localized periodontitis.
  • In this report, we present a case of disseminated Langerhans' cell histiocytosis in a 30-month-old boy who had a mass covering the entire maxillopalatine region and suffered severe periodontal destruction in the posterior maxilla and mandible.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / radiography. Mandibular Diseases / radiography. Maxillary Diseases / radiography
  • [MeSH-minor] Child, Preschool. Diagnosis, Differential. Humans. Male. Treatment Outcome

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  • (PMID = 18033951.001).
  • [ISSN] 0250-832X
  • [Journal-full-title] Dento maxillo facial radiology
  • [ISO-abbreviation] Dentomaxillofac Radiol
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] England
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34. Hermans G, Wilmer A, Knockaert D, Meyns B: Endogenous carbon monoxide production: a rare and detrimental complication of extracorporeal membrane oxygenation. ASAIO J; 2008 Nov-Dec;54(6):633-5
Hazardous Substances Data Bank. Carbon monoxide .

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  • Extracorporeal membrane oxygenation (ECMO) is a technique that can support gas-exchange and cardiac function in patients with acute respiratory or cardiac failure that is not responsive to conservative treatment.
  • We report on a patient with end-stage pulmonary fibrosis (histiocytosis x), in whom ECMO was used as bridge to urgent lung transplantation.

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  • (PMID = 19033779.001).
  • [ISSN] 1538-943X
  • [Journal-full-title] ASAIO journal (American Society for Artificial Internal Organs : 1992)
  • [ISO-abbreviation] ASAIO J.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] United States
  • [Chemical-registry-number] 7U1EE4V452 / Carbon Monoxide; 9061-29-4 / Carboxyhemoglobin
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35. Medina R, Domingo ML, Calvillo P, Martínez M, Vilar J: [Smoking-related interstitial lung diseases: findings at high-resolution CT]. Radiologia; 2008 Jul-Aug;50(4):317-22
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Transliterated title] Enfermedades intersticiales relacionadas con el tabaco: hallazgos en TC de alta resolución.
  • MATERIAL AND METHODS: We reviewed the clinical histories of patients with suspected smoking-related interstitial lung diseases from 2001 to 2005 who underwent high-resolution computed tomography and had radiologic findings of desquamative interstitial pneumonia, respiratory bronchiolitis, histiocytosis X, or pulmonary fibrosis.
  • In desquamative interstitial pneumonia, the most common finding was ground glass (100%); in respiratory bronchiolitis, it was centrilobar nodules (100%); cysts were the most common finding in histiocytosis (85.7%) and honey combing was the most common finding in fibrosis (100%).
  • CONCLUSIONS: There is a relation between smoking and these interstitial diseases, as well as overlapping in their clinical and radiological manifestations.

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  • (PMID = 18783653.001).
  • [ISSN] 0033-8338
  • [Journal-full-title] Radiología
  • [ISO-abbreviation] Radiologia
  • [Language] spa
  • [Publication-type] English Abstract; Journal Article
  • [Publication-country] Spain
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36. Barron MJ, McDonnell ST, Mackie I, Dixon MJ: Hereditary dentine disorders: dentinogenesis imperfecta and dentine dysplasia. Orphanet J Rare Dis; 2008;3:31
SciCrunch. KEGG: Data: Disease Annotation .

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  • Diagnosis is based on family history, pedigree construction and detailed clinical examination, while genetic diagnosis may become useful in the future once sufficient disease-causing mutations have been discovered.
  • Differential diagnoses include hypocalcified forms of amelogenesis imperfecta, congenital erythropoietic porphyria, conditions leading to early tooth loss (Kostmann's disease, cyclic neutropenia, Chediak-Hegashi syndrome, histiocytosis X, Papillon-Lefevre syndrome), permanent teeth discolouration due to tetracyclines, Vitamin D-dependent and vitamin D-resistant rickets.
  • Beginning in infancy, treatment usually continues into adulthood with a number of options including the use of crowns, over-dentures and dental implants depending on the age of the patient and the condition of the dentition.
  • Where diagnosis occurs early in life and treatment follows the outlined recommendations, good aesthetics and function can be obtained.

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  • (PMID = 19021896.001).
  • [ISSN] 1750-1172
  • [Journal-full-title] Orphanet journal of rare diseases
  • [ISO-abbreviation] Orphanet J Rare Dis
  • [Language] eng
  • [Publication-type] Journal Article; Review
  • [Publication-country] England
  • [Chemical-registry-number] 0 / Extracellular Matrix Proteins; 0 / Phosphoproteins; 0 / Sialoglycoproteins; 0 / dentin sialophosphoprotein
  • [Number-of-references] 72
  • [Other-IDs] NLM/ PMC2600777
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37. Horn EM, Coons SW, Spetzler RF, Rekate HL: Isolated Langerhans cell histiocytosis of the infundibulum presenting with fulminant diabetes insipidus. Childs Nerv Syst; 2006 May;22(5):542-4
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Isolated Langerhans cell histiocytosis of the infundibulum presenting with fulminant diabetes insipidus.
  • INTRODUCTION: Langerhans cell histiocytosis (histiocytosis X) is a rare disorder that can manifest with solitary bony lesions or disseminated disease in various tissues.
  • A common manifestation of the disease is diabetes insipidus even in the absence of neural involvement.
  • Disseminated disease often involves the central nervous system, but only six isolated lesions in the infundibulum have been reported.
  • Microscopic analysis showed multiple lymphocytes and eosinophils with Langerhans cells that stained positive for S-100.
  • Langerhans cell histiocytosis was diagnosed, and the patient was discharged on postoperative day 6 with no neurological deficits.
  • CONCLUSIONS: Isolated Langerhans cell histiocytosis of the infundibulum is rare.
  • [MeSH-major] Diabetes Insipidus / complications. Histiocytosis, Langerhans-Cell / complications


38. Zhong WQ, Jiang L, Ma QJ, Liu ZJ, Liu XG, Wei F, Yuan HS, Dang GT: Langerhans cell histiocytosis of the atlas in an adult. Eur Spine J; 2010 Jan;19(1):19-22
MedlinePlus Health Information. consumer health - Spine Injuries and Disorders.

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Langerhans cell histiocytosis of the atlas in an adult.
  • Langerhans cell histiocytosis (LCH), formerly known as histiocytosis X, is a rare disorder (approximately 1:1,500,000 inhabitants) characterized by clonal proliferation and excess accumulation of pathologic Langerhans cells causing local or systemic effects.
  • The most frequent sites of the bony lesions are the skull, femur, mandible, pelvis and spine.
  • Histopathological diagnosis was Langerhans cell histiocytosis by percutaneous needle biopsy under CT guidance.
  • [MeSH-major] Cervical Atlas / pathology. Cervical Atlas / radiography. Histiocytosis, Langerhans-Cell / diagnosis. Histiocytosis, Langerhans-Cell / therapy. Spinal Diseases / diagnosis. Spinal Diseases / therapy

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  • (PMID = 19844749.001).
  • [ISSN] 1432-0932
  • [Journal-full-title] European spine journal : official publication of the European Spine Society, the European Spinal Deformity Society, and the European Section of the Cervical Spine Research Society
  • [ISO-abbreviation] Eur Spine J
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article; Review
  • [Publication-country] Germany
  • [Number-of-references] 21
  • [Other-IDs] NLM/ PMC2899733
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39. Fadel E, Mercier O, Mussot S, Leroy-Ladurie F, Cerrina J, Chapelier A, Simonneau G, Dartevelle P: Long-term outcome of double-lung and heart-lung transplantation for pulmonary hypertension: a comparative retrospective study of 219 patients. Eur J Cardiothorac Surg; 2010 Sep;38(3):277-84
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  • At our institution, patients with severe right ventricular dysfunction or congenital systemic-to-pulmonary shunt (CSPS) are preferentially treated with HLT.
  • According to the new clinical classification of PH, 147 patients were group I (pulmonary arterial hypertension group, of which 30 had CSPS), 24 were group III (PH associated with lung disease and/or hypoxaemia), 20 were group IV (chronic thrombo-embolic PH) and 20 were group V (sarcoidosis or histiocytosis X).
  • RESULTS: Compared with the HLT group, the DLT group had less severe disease as reflected by a higher preoperative cardiac index (2.5 + or - 0.8 vs 2.0 + or - 0.4; P=0.0006), lower New York Heart Association (NYHA) functional class (3.4 + or - 0.4 vs 3.8 + or - 0.5; P<0.0001), lower rates of kidney failure (31% vs 66%; P<0.0001) and liver failure (13% vs 38%; P=0.0003) and less need for preoperative inotropic support (10% vs 25%; P=0.014).

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  • [Copyright] Copyright 2010 European Association for Cardio-Thoracic Surgery. Published by Elsevier B.V. All rights reserved.
  • (PMID = 20371187.001).
  • [ISSN] 1873-734X
  • [Journal-full-title] European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery
  • [ISO-abbreviation] Eur J Cardiothorac Surg
  • [Language] eng
  • [Publication-type] Comparative Study; Journal Article
  • [Publication-country] Germany
  • [Chemical-registry-number] 0 / Immunosuppressive Agents
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40. Sorichter S, Baumann U, Baumgart A, Walterspacher S, von Specht BU: Immune responses in the airways by nasal vaccination with systemic boosting against Pseudomonas aeruginosa in chronic lung disease. Vaccine; 2009 May 11;27(21):2755-9
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Immune responses in the airways by nasal vaccination with systemic boosting against Pseudomonas aeruginosa in chronic lung disease.
  • Systemic vaccination in patients with cystic fibrosis has been only successful in part.
  • METHODS: 12 patients with chronic lung diseases (8 COPD, 2 cystic fibrosis, 1 bronchiectasis, 1 histiocytosis X) were vaccinated three times intranasally followed by a systemic booster vaccination with a recombinant hybrid protein encompassing the main protective epitopes of two outer membrane proteins of P. aeruginosa.
  • Mucosal and systemic antibody responses were measured after boosting and after a half-year follow-up compared to a representative control cohort.
  • CONCLUSIONS: Mucosal vaccination followed by systemic boost with an outer membrane protein vaccine against P. aeruginosa leads to airway immunogenicity against the pathogen.
  • Further clinical trials should elucidate the protective efficacy of this vaccination method.
  • [MeSH-minor] Administration, Intranasal. Adult. Aged. Antibodies, Viral / immunology. Chronic Disease. Female. Humans. Male. Middle Aged. Nasal Mucosa / immunology

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  • (PMID = 19366571.001).
  • [ISSN] 0264-410X
  • [Journal-full-title] Vaccine
  • [ISO-abbreviation] Vaccine
  • [Language] eng
  • [Publication-type] Clinical Trial, Phase I; Clinical Trial, Phase II; Journal Article; Research Support, Non-U.S. Gov't
  • [Publication-country] Netherlands
  • [Chemical-registry-number] 0 / Antibodies, Viral; 0 / Pseudomonas Vaccines
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41. Wutzl A, Eisenmenger G, Hoffmann M, Czerny C, Moser D, Pietschmann P, Ewers R, Baumann A: Osteonecrosis of the jaws and bisphosphonate treatment in cancer patients. Wien Klin Wochenschr; 2006 Aug;118(15-16):473-8
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  • RESULTS: The reasons for bisphosphonate treatment were multiple myeloma in 12 patients, breast cancer with bone metastasis in four patients and histiocytosis X in one patient.
  • Clinical symptoms were exposed bone, pain and local inflammation of the mucosa.
  • [MeSH-minor] Adult. Aged. Biopsy. Female. Follow-Up Studies. Histiocytosis, Langerhans-Cell / drug therapy. Humans. Injections, Intravenous. Magnetic Resonance Imaging. Male. Mandible / pathology. Mandibular Diseases / chemically induced. Mandibular Diseases / diagnosis. Mandibular Diseases / pathology. Mandibular Diseases / radiography. Mandibular Diseases / radionuclide imaging. Mandibular Diseases / surgery. Maxilla / pathology. Maxillary Diseases / chemically induced. Maxillary Diseases / diagnosis. Maxillary Diseases / pathology. Maxillary Diseases / radiography. Maxillary Diseases / radionuclide imaging. Maxillary Diseases / surgery. Middle Aged. Radiography, Panoramic. Retrospective Studies. Risk Factors. Time Factors. Tomography, X-Ray Computed

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  • (PMID = 16957978.001).
  • [ISSN] 0043-5325
  • [Journal-full-title] Wiener klinische Wochenschrift
  • [ISO-abbreviation] Wien. Klin. Wochenschr.
  • [Language] eng
  • [Publication-type] Comparative Study; Journal Article
  • [Publication-country] Austria
  • [Chemical-registry-number] 0 / Bone Density Conservation Agents; 0 / Diphosphonates; 0 / Imidazoles; 6XC1PAD3KF / zoledronic acid; OYY3447OMC / pamidronate
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42. Rolland A, Guyon L, Gill M, Cai YH, Banchereau J, McClain K, Palucka AK: Increased blood myeloid dendritic cells and dendritic cell-poietins in Langerhans cell histiocytosis. J Immunol; 2005 Mar 1;174(5):3067-71
The Lens. Cited by Patents in .

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Increased blood myeloid dendritic cells and dendritic cell-poietins in Langerhans cell histiocytosis.
  • Langerhans cell histiocytosis (LCH), previously known as histiocytosis X, is a reactive proliferative disease of unknown pathogenesis.
  • Because multiple APCs, including Langerhans cells and macrophages, are involved in the lesion formation, we surmised that LCH is a disease of myeloid blood precursors.
  • We found that lin(-) HLA-DR(+)CD11c-+ precursors of dendritic cells, able to give rise to either Langerhans cells or macrophages, are significantly (p = 0.004) increased in the blood of LCH patients.
  • The analysis of serum cytokines in 24 patients demonstrated significantly elevated levels of hemopoietic cytokines such as fms-like tyrosine kinase ligand (FLT3-L, a dendritic cell-mobilizing factor, approximately 2-fold) and M-CSF ( approximately 4-fold).
  • Higher levels of these cytokines correlated with patients having more extensive disease.
  • Finally, patients with bone lesions had relatively higher levels of M-CSF and of stem cell factor.
  • Thus, early hemopoietic cytokines such as FLT3-L, stem cell factor, and M-CSF maybe relevant in LCH pathogenesis and might be considered as novel therapeutic targets.
  • [MeSH-major] Dendritic Cells / metabolism. Dendritic Cells / pathology. Hematopoietic Cell Growth Factors / blood. Histiocytosis, Langerhans-Cell / blood. Histiocytosis, Langerhans-Cell / pathology. Myeloid Cells / metabolism. Myeloid Cells / pathology
  • [MeSH-minor] Adult. Child. Cytokines / biosynthesis. Cytokines / blood. Humans. Leukocyte Count. Ligands. Macrophage Colony-Stimulating Factor / biosynthesis. Macrophage Colony-Stimulating Factor / blood. Membrane Proteins / biosynthesis. Membrane Proteins / blood. Myeloid Progenitor Cells / immunology. Myeloid Progenitor Cells / metabolism. Myeloid Progenitor Cells / pathology. Pilot Projects. Stem Cell Factor / biosynthesis. Stem Cell Factor / blood

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  • (PMID = 15728521.001).
  • [ISSN] 0022-1767
  • [Journal-full-title] Journal of immunology (Baltimore, Md. : 1950)
  • [ISO-abbreviation] J. Immunol.
  • [Language] eng
  • [Grant] United States / NCI NIH HHS / CA / CA78846
  • [Publication-type] Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.
  • [Publication-country] United States
  • [Chemical-registry-number] 0 / Cytokines; 0 / Hematopoietic Cell Growth Factors; 0 / Ligands; 0 / Membrane Proteins; 0 / Stem Cell Factor; 0 / flt3 ligand protein; 81627-83-0 / Macrophage Colony-Stimulating Factor
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43. Oudidi A, Hachimi H, El Alami MN: [Langerhans cell histiocytosis of the thyroid]. Presse Med; 2006 Jun;35(6 Pt 1):977-9
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  • [Title] [Langerhans cell histiocytosis of the thyroid].
  • [Transliterated title] Histiocytose langerhansienne de la thyroïde.
  • INTRODUCTION: Langerhans cell histiocytosis, also known as histiocytosis X, has a broad clinical spectrum and highly variable prognosis.
  • Immunohistochemical and pathology analyses showed Langerhans cell histiocytosis of the thyroid.
  • CONCLUSION: Diagnosis and treatment of Langerhans cell histiocytosis in the thyroid gland often require multidisciplinary cooperation to analyze clinical, radiological, and pathology findings.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / pathology. Thyroid Gland / pathology

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  • (PMID = 16783257.001).
  • [ISSN] 0755-4982
  • [Journal-full-title] Presse medicale (Paris, France : 1983)
  • [ISO-abbreviation] Presse Med
  • [Language] fre
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] France
  • [Chemical-registry-number] 9002-71-5 / Thyrotropin
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44. Gun F, Toker A, Kaya S, Tanju S, Dilege S, Celik A, Salman T, Yilmazbayhan D: Cervical mediastinoscopy for paratracheal masses in pediatric patients. Pediatr Hematol Oncol; 2008 Jun;25(5):393-7

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  • A cytological diagnosis is essential for a definitive diagnosis in children who have paratracheal lesions.
  • Age, gender, preoperative diagnosis, and postoperative biopsy results and complications were reviewed.
  • Five patients had mediastinal lesions residuing or recurring after chemotherapy for either Hodgkin disease or non-Hodgkin lymphoma.
  • In 2 of these patients, the diagnosis was recurrent disease.
  • Among the 8 patients presenting with a paratracheal mass or enlarged lymph nodes, histopathologic diagnosis showed tuberculosis in 3 children, Hodgkin disease in 2 children, and histiocytosis X and non-Hodgkin lymphoma 1 patient in each.
  • This study shows that cervical mediastinoscopy gave 100% correct diagnosis for mediastinal residual malignancies or uncommon forms of mycobacterium tuberculosis with paratracheal masses.
  • [MeSH-major] Mediastinal Neoplasms / diagnosis. Mediastinoscopy / standards
  • [MeSH-minor] Adolescent. Biopsy. Child. Child, Preschool. Female. Histiocytosis, Langerhans-Cell. Humans. Lymphoma / complications. Lymphoma / drug therapy. Male. Neoplasms, Second Primary / diagnosis. Retrospective Studies. Tuberculosis

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  • (PMID = 18569841.001).
  • [ISSN] 1521-0669
  • [Journal-full-title] Pediatric hematology and oncology
  • [ISO-abbreviation] Pediatr Hematol Oncol
  • [Language] eng
  • [Publication-type] Evaluation Studies; Journal Article
  • [Publication-country] England
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45. Bendayan D, Shitrit D, Kramer MR: Combination therapy with prostacyclin and tadalafil for severe pulmonary arterial hypertension: a pilot study. Respirology; 2008 Nov;13(6):916-8
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  • Two patients had Eisenmenger syndrome, one had pulmonary hypertension associated with scleroderma and one had histiocytosis X.
  • Tadalafil may be beneficial for the treatment of patients with advanced disease.


46. Szlubowski A, Soja J, Grzanka P, Tomaszewska R, Papla B, Kuzdzał J, Cmiel A, Sładek K: TGF-beta1 in bronchoalveolar lavage fluid in diffuse parenchymal lung diseases and high-resolution computed tomography score. Pol Arch Med Wewn; 2010 Jul;120(7-8):270-5
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  • INTRODUCTION: In the pathogenesis of diffuse parenchymal lung diseases (DPLDs), growth factors, including transforming growth factor beta1 (TGF-beta1), are responsible for cell proliferation, apoptosis, chemotaxis, and angiogenesis, and also for the production and secretion of some components of the extracellular matrix.
  • RESULTS: All 31 patients were diagnosed, and based on histopathology, they were classified into 2 groups: idiopathic interstitial pneumonia (usual interstitial pneumonia - 12, nonspecific inter stitial pneumonia - 2, cryptogenic organizing pneumonia - 2, and desquamative interstitial pneumonia - 1) and granulomatous disease (sarcoidosis - 7, extrinsic allergic alveolitis - 5, and histiocytosis X - 2).

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  • (PMID = 20693957.001).
  • [ISSN] 1897-9483
  • [Journal-full-title] Polskie Archiwum Medycyny Wewnetrznej
  • [ISO-abbreviation] Pol. Arch. Med. Wewn.
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] Poland
  • [Chemical-registry-number] 0 / Transforming Growth Factor beta1
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47. Moralis A, Kunkel M, Kleinsasser N, Müller-Richter U, Reichert TE, Driemel O: Intralesional corticosteroid therapy for mandibular Langerhans cell histiocytosis preserving the intralesional tooth germ. Oral Maxillofac Surg; 2008 Jul;12(2):105-11
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  • [Title] Intralesional corticosteroid therapy for mandibular Langerhans cell histiocytosis preserving the intralesional tooth germ.
  • BACKGROUND: Langerhans cell histiocytosis (LCH, histiocytosis X, ICD-O 9751/1) refers to a neoplastic proliferation of Langerhans cells.
  • The course of the disease determines the treatment and prognosis.
  • PURPOSE: Presentation of our own case will review LCH, a very rare disease entity in oral-facial surgery and will document that intralesional corticosteroid injection is a less invasive alternative to the classical surgical curettage and local radiation therapy.
  • CASE REPORT: In a 10-year-old boy, a progressive, pressure-sensitive swelling had developed within 1 week in the left paramandibular and submandibular area.
  • [MeSH-major] Glucocorticoids / administration & dosage. Histiocytosis, Langerhans-Cell / drug therapy. Mandibular Diseases / drug therapy. Methylprednisolone / administration & dosage

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  • (PMID = 18594882.001).
  • [ISSN] 1865-1550
  • [Journal-full-title] Oral and maxillofacial surgery
  • [ISO-abbreviation] Oral Maxillofac Surg
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Germany
  • [Chemical-registry-number] 0 / Anti-Inflammatory Agents; 0 / Glucocorticoids; X4W7ZR7023 / Methylprednisolone
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48. Vernaeve V, Bodri D, Colodrón M, Vidal R, Durbán M, Coll O: Endometrial receptivity after oocyte donation in recipients with a history of chemotherapy and/or radiotherapy. Hum Reprod; 2007 Nov;22(11):2863-7
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  • RESULTS: The primary diseases of the patients were Hodgkin's lymphoma (n = 12), non-Hodgkin's lymphoma (n = 3), leukaemia (n = 7), ovarian cancer (n = 6), Ewing's sarcoma (n = 2), breast cancer (n = 1), sympathoblastoma (n = 1) and histiocytosis X (n = 1).

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  • (PMID = 17855411.001).
  • [ISSN] 0268-1161
  • [Journal-full-title] Human reproduction (Oxford, England)
  • [ISO-abbreviation] Hum. Reprod.
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] England
  • [Chemical-registry-number] 0 / Antineoplastic Agents
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49. Li Z, Li ZB, Zhang W, Li JR, Wang SP, Cheng Y, Wei MX: Eosinophilic granuloma of the jaws: an analysis of clinical and radiographic presentation. Oral Oncol; 2006 Jul;42(6):574-80
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  • [Title] Eosinophilic granuloma of the jaws: an analysis of clinical and radiographic presentation.
  • Eosinophilic granuloma (EG) is the localized and mildest form of histiocytosis-X group of diseases.
  • In this study, 22 patients of pathologically proven EG involving the jaws were retrospectively studied concerning the clinical and radiographic presentation.
  • The clinical and radiographic presentation of the 22 cases was quite varied, and the accuracy of clinical and radiographic diagnosis was low.
  • However, the clinical and radiographic presentation correlated with the lesion site, and accordingly all the jaw lesions could be divided into three types (Alveolar Type, Intraosseous Type, and Mixed Type).
  • Our classification based on the lesion sites reveals the correlation between the clinical and radiographic presentation of EG and the lesion sites, and may be useful in the identification of lesions of EG in the jaws.
  • [MeSH-major] Eosinophilic Granuloma / diagnosis. Jaw Diseases / diagnosis

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  • (PMID = 16469529.001).
  • [ISSN] 1368-8375
  • [Journal-full-title] Oral oncology
  • [ISO-abbreviation] Oral Oncol.
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] England
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50. Mengistu AD, Bedri A, Schneider J: Unifocal langerhans cell histiocytosis presenting with pathological fracture. Ethiop Med J; 2007 Jan;45(1):91-3
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  • [Title] Unifocal langerhans cell histiocytosis presenting with pathological fracture.
  • The patient was initially treated as a case of osteomyelitis until the diagnosis of Langerhans cell histiocytosis (histiocytosis X, eosiniphilic granuloma) was made by bone biopsy.
  • The clinical presentation of the case and brief review of the literature is discussed.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / pathology
  • [MeSH-minor] Adolescent. Adrenal Cortex Hormones / therapeutic use. Diagnosis, Differential. Female. Humans

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  • (PMID = 17642163.001).
  • [ISSN] 0014-1755
  • [Journal-full-title] Ethiopian medical journal
  • [ISO-abbreviation] Ethiop. Med. J.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Ethiopia
  • [Chemical-registry-number] 0 / Adrenal Cortex Hormones
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51. Mignogna MD, Fedele S, Lo Russo L, Lanza A, Marenzi G, Sammartino G: Gorham's disease of the mandible mimicking periodontal disease on radiograph. J Clin Periodontol; 2005 Sep;32(9):1022-6
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  • [Title] Gorham's disease of the mandible mimicking periodontal disease on radiograph.
  • BACKGROUND: Gorham's disease is a rare disorder characterized by spontaneous and progressive osteolysis of one or more skeletal bones.
  • The radiographic findings associated with Gorham's disease are particularly dramatic, as in some cases a complete resorption of the involved bone can occur, leading to the definition of phantom bone, vanishing bone, or disappearing bone disease.
  • MATERIAL AND METHODS: A 24-year-old female patient with a previous diagnosis of periodontal disease and progressive mandibular alveolar bone loss was referred to our Oral Medicine section.
  • RESULTS: After further extensive local and systemic evaluation, including histopathological, laboratory and imagine techniques investigations, the patient was diagnosed to be affected by Gorham's disease.
  • Appropriate medical therapy was successful in stabilizating the resorptive process, with no evidence of further progressive disease.
  • CONCLUSIONS: When Gorham's disease involves the mandible, the role of the periodontologist is extremely important in diagnosing promptly the disorder and preventing the functional and aesthetic consequences of advanced and extensive bone loss.
  • Gorham's disease should be included among the pathologic entities mimicking periodontal disease on radiograph, such as inflammatory disease (e.g. osteomyelitis), endocrine disease (e.g. hyperparathyroidism), intra-osseous malignancies or metastases, lymphoma, histiocytosis X, mainly eosinophilic granuloma, infective process (e.g. tuberculosis and actinomycosis), odontogenic tumours.
  • [MeSH-minor] Adult. Diagnosis, Differential. Diphosphonates / therapeutic use. Female. Humans. Imidazoles / therapeutic use. Tomography, X-Ray Computed

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  • (PMID = 16104969.001).
  • [ISSN] 0303-6979
  • [Journal-full-title] Journal of clinical periodontology
  • [ISO-abbreviation] J. Clin. Periodontol.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Denmark
  • [Chemical-registry-number] 0 / Diphosphonates; 0 / Imidazoles; 6XC1PAD3KF / zoledronic acid
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52. Hanif G, Ali SI, Shahid A, Rehman F, Mirza U: Role of biopsy in pediatric lymphadenopathy. Saudi Med J; 2009 Jun;30(6):798-802
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  • OBJECTIVE: To determine the role of lymph node biopsy in the diagnosis of lymphadenopathy and to find out the pattern of different diseases in relation to age, gender, and the site of lymph nodes involved.
  • Tissue samples were collected from 898 children presenting with lymphadenopathy, and the diagnosis was confirmed on histology and through various specific tests.
  • The clinical data of the patients were collected from computerized hospital records.
  • The rest of the lesions include; 72 cases of granulomatous lymphadenitis (8%), 13 of histiocytosis X (1.4%), 44 (4.9%) of metastatic tumors, 16 of chronic inflammation (1.8%), and 3 cases of Kikuchi's disease (0.3%).
  • The cause of lymphadenopathy was found to be significantly associated with age, gender, and site of the lymph nodes involved.
  • Although 39.6% of children had reactive hyperplasia of unknown etiology, 60.3% children presented with a specific diagnosis.

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  • [CommentIn] Saudi Med J. 2010 Feb;31(2):215 [20174747.001]
  • (PMID = 19526163.001).
  • [ISSN] 0379-5284
  • [Journal-full-title] Saudi medical journal
  • [ISO-abbreviation] Saudi Med J
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] Saudi Arabia
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53. Orzechowska-Wylegała B, Niedzielska I, Sobol G: [Langerhans' cell histiocytosis--diagnostic and treatment difficulties]. Pol Merkur Lekarski; 2008 May;24(143):439-42
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  • [Title] [Langerhans' cell histiocytosis--diagnostic and treatment difficulties].
  • Langerhans' cell histiocytosis [(LCH), histiocytosis X] is a very rare disease, which can involve any side and organ of the body.
  • LCH may appear as an isolated leasion or as a widespread systemic disease.
  • Focus in the bone as eosinophilic granuloma can be separate or be involved only as a part of generalized disease.
  • After diagnosis child was treatment by chemotherapy and stay in remission.
  • In differential diagnosis of infiltrations and osteolytic losses of maxilla and mandible one should take into account LCH.
  • 2. Differential localization and non characteristic symptoms can cause the late diagnosis and aggravate the prognosis of this severe disease.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / diagnosis. Histiocytosis, Langerhans-Cell / drug therapy

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  • (PMID = 18634391.001).
  • [ISSN] 1426-9686
  • [Journal-full-title] Polski merkuriusz lekarski : organ Polskiego Towarzystwa Lekarskiego
  • [ISO-abbreviation] Pol. Merkur. Lekarski
  • [Language] pol
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] Poland
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54. Lang-Lazdunski L, Pilling J: Videothoracoscopic excision of mediastinal tumors and cysts using the harmonic scalpel. Thorac Cardiovasc Surg; 2008 Aug;56(5):278-82

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  • Histopathology revealed 1 esophageal leiomyosarcoma, 1 Langerhans cell histiocytosis X, 1 hamartoma, 5 schwannomas, 1 neurofibroma, 1 malignant peripheral nerve sheath tumor, 1 reactive lymphadenopathy, 1 tuberculous lymphadenopathy, 1 cystic hygroma, 2 bronchogenic cysts, 2 foregut cysts, 1 thymic cyst, and 1 pleuropericardial cyst.

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  • (PMID = 18615374.001).
  • [ISSN] 0171-6425
  • [Journal-full-title] The Thoracic and cardiovascular surgeon
  • [ISO-abbreviation] Thorac Cardiovasc Surg
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] Germany
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55. Sperandeo M, Sperandeo G, Varriale A, Filabozzi P, Decuzzi M, Dimitri L, Vendemiale G: Contrast-enhanced ultrasound (CEUS) for the study of peripheral lung lesions: a preliminary study. Ultrasound Med Biol; 2006 Oct;32(10):1467-72
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  • All FNBs performed under CEUS guidance were adequate for pathologic diagnosis.
  • Seventy-eight lesions were malignant: 33 (41.9%) were adenocarcinomas, 29 (36.5%) were squamous-cell carcinomas, 13 (17.6%) were undifferentiated large-cell carcinomas and the remaining three (4.1%) were small-cell carcinomas.
  • The other 20 lesions were benign (four lipomas, two fibrous lung tumor, two noncaseous granulomas, six abscesses, one rheumatoid nodule, one histiocytosis X, one chondroid hamartoma, one sclerosing hemangioma, two sarcoid nodules) and none presented intralesional enhancement.
  • [MeSH-minor] Adenocarcinoma / ultrasonography. Aged. Biopsy, Fine-Needle / methods. Carcinoma, Large Cell / ultrasonography. Carcinoma, Small Cell / ultrasonography. Carcinoma, Squamous Cell / ultrasonography. Contrast Media. Female. Humans. Image Enhancement / methods. Male. Microbubbles. Middle Aged. Phospholipids. Sulfur Hexafluoride

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  • (PMID = 17045865.001).
  • [ISSN] 0301-5629
  • [Journal-full-title] Ultrasound in medicine & biology
  • [ISO-abbreviation] Ultrasound Med Biol
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] England
  • [Chemical-registry-number] 0 / Contrast Media; 0 / Phospholipids; 0 / contrast agent BR1; WS7LR3I1D6 / Sulfur Hexafluoride
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56. Chatterjee T, Naithani R, Agrawal N, Bhattacharya J, Bhattacharya M, Dutta P, Pati HP, Mahapatra M, Choudhary VP: Disseminated Langerhans cell histiocytosis-an interesting case report with concise review of literature. Indian J Pathol Microbiol; 2006 Apr;49(2):248-50
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  • [Title] Disseminated Langerhans cell histiocytosis-an interesting case report with concise review of literature.
  • He was diagnosed as disseminated langerhans cell histiocytosis.
  • The occurrence of histiocytosis is reviewed and possible treatment is discussed.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / diagnosis

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  • (PMID = 16933727.001).
  • [ISSN] 0377-4929
  • [Journal-full-title] Indian journal of pathology & microbiology
  • [ISO-abbreviation] Indian J Pathol Microbiol
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article; Review
  • [Publication-country] India
  • [Chemical-registry-number] 0 / Antigens, CD; 0 / Antigens, CD1; 0 / Antigens, Differentiation, Myelomonocytic; 0 / CD1a antigen; 0 / CD68 antigen, human; 0 / S100 Proteins
  • [Number-of-references] 18
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57. Jellinger KA: A short history of neurosciences in Austria. J Neural Transm (Vienna); 2006 Mar;113(3):271-82

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  • Schüller (histiocytosis X), C. v. Economo (encephalitis lethargica and cytoarchitectonics of the human cerebral cortex), E.
  • Pollak (Wilson disease), E.
  • Important for the future are the foundation of the Institute of Brain Research at Vienna Medical University and of the Austrian Society of Neurology which will give further impact for the future progress of neuroscience research in Austria and its integration into the international science community.

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  • (PMID = 16453085.001).
  • [ISSN] 0300-9564
  • [Journal-full-title] Journal of neural transmission (Vienna, Austria : 1996)
  • [ISO-abbreviation] J Neural Transm (Vienna)
  • [Language] eng
  • [Publication-type] Historical Article; Journal Article; Portraits
  • [Publication-country] Austria
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58. Hoover KB, Rosenthal DI, Mankin H: Langerhans cell histiocytosis. Skeletal Radiol; 2007 Feb;36(2):95-104
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  • [Title] Langerhans cell histiocytosis.
  • Langerhans cell histiocytosis (LCH) is a complex disease entity comprised of three distinct clinical syndromes that demonstrate indistinguishable histology.
  • These syndromes are: eosinophilic granuloma, which is predominantly osseous or pulmonary; Hand-Schûller-Christian's disease, which involves multiple organ systems and, most typically, the skull base; and Letterer-Siwe's disease, the most severe disease manifestation, which typically involves the abdominal viscera.
  • This article reviews our current understanding of Langerhans cell histiocytosis by discussing the history, histology, etiology, and treatment of the disease.
  • It focuses on the radiographic findings and imaging modalities that are the most useful in disease diagnosis and management.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / diagnosis. Histiocytosis, Langerhans-Cell / therapy. Magnetic Resonance Imaging / methods. Tomography, X-Ray Computed / methods


59. Abi Khalil S, Gourdier AL, Aoun N, Nedelcu C, El Rai S, Moubarak E, Sfeir S, Willoteaux S, Aubé C: [Cystic and cavitary lesions of the lung: imaging characteristics and differential diagnosis]. J Radiol; 2010 Apr;91(4):465-73
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  • [Title] [Cystic and cavitary lesions of the lung: imaging characteristics and differential diagnosis].
  • Gas containing lesions of the lung can be differentiated into cystic and cavitary lesions based on their imaging characteristics, which is helpful for differential diagnosis.
  • The differential diagnosis includes: histiocytosis X, lymphangioleiomyomatosis, cystic metastases, septic emboli, pulmonary sequestration.
  • [MeSH-minor] Diagnosis, Differential. Histiocytosis, Langerhans-Cell / radiography. Humans. Image Processing, Computer-Assisted / methods. Lung / abnormalities. Lung Abscess / radiography. Lung Diseases, Fungal / radiography. Lung Diseases, Interstitial / radiography. Lung Neoplasms / radiography. Lymphangioleiomyomatosis / radiography. Sarcoidosis, Pulmonary / radiography

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  • (PMID = 20514002.001).
  • [ISSN] 0221-0363
  • [Journal-full-title] Journal de radiologie
  • [ISO-abbreviation] J Radiol
  • [Language] fre
  • [Publication-type] English Abstract; Journal Article
  • [Publication-country] France
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60. Zofková I: [Pathogenetically complicated case of osteoporosis in a young man]. Cas Lek Cesk; 2008;147(11):574-8
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  • Osteoporosis, is a serious disease both in women and men, with a high risk of fractures.
  • The aim of this case study is to demonstrate the complex pathogenesis of a severe osteoporosis in a 23-year-old heavy smoker with histiocytosis X, diabetes insipidus (DI), subclinical hypogonadism and low serum levels of IGF-I.
  • On the other hand, a direct causal association between histiocytosis X and osteoporosis was not confirmed histomorphometrically in this patient.
  • [MeSH-minor] Adult. Histiocytosis, Langerhans-Cell / complications. Humans. Male. Young Adult

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  • (PMID = 19097362.001).
  • [ISSN] 0008-7335
  • [Journal-full-title] Casopís lékar̆ů c̆eských
  • [ISO-abbreviation] Cas. Lek. Cesk.
  • [Language] cze
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] Czech Republic
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61. Mathis S, Levillain P, Vandermarcq P, Gil R, Auche V, Ciron J, Neau JP: [Solitary intracerebral langerhans cell histiocytosis: report of one case and literature review]. Rev Med Interne; 2007 Sep;28(9):645-50
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  • [Title] [Solitary intracerebral langerhans cell histiocytosis: report of one case and literature review].
  • [Transliterated title] Histiocytose langerhansienne encéphalique isolée à forme pseudotumorale: une observation et revue de la littérature.
  • INTRODUCTION: Langerhans cell histiocytosis is a multivisceral pathology.
  • EXEGESIS: We report the case of a 31 year old man hospitalized for left partial motor seizure revealing a right frontal tumor with criteria for histiocytosis X.
  • The histological and biological examination found criteria for Langerhans cell histiocytosis (CD1a and S100 reactivity).
  • The check-up for extracerebral localisations of the disease was negative.
  • The review of the literature and a discussion on neurological manifestations of this disease were carried out.
  • CONCLUSION: A neurological manifestation can be the first and only symptom of a Langerhans cell histiocytosis.

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  • (PMID = 17566611.001).
  • [ISSN] 0248-8663
  • [Journal-full-title] La Revue de medecine interne
  • [ISO-abbreviation] Rev Med Interne
  • [Language] FRE
  • [Publication-type] Case Reports; English Abstract; Journal Article; Review
  • [Publication-country] France
  • [Chemical-registry-number] 0 / Antigens, CD1; 0 / CD1a antigen
  • [Number-of-references] 43
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62. Tinsa F, Brini I, Kharfi M, Mrad K, Boussetta K, Bousnina S: Perianal presentation of Langerhans cell histiocytosis in children. Gastroenterol Clin Biol; 2010 Jan;34(1):95-7
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Perianal presentation of Langerhans cell histiocytosis in children.
  • Langerhans cell histiocytosis, previously known as histiocytosis X, is a disease whose clinical presentation varies.
  • Although it is uncommon, Langerhans cell histiocytosis may involve the perianal region.
  • We report the case of a 2-year-old boy who presented with perianal ulcerated vegetative lesions and seborrheic dermatitis of the scalp.
  • Biopsy of the lesions showed Langerhans cell histiocytosis.
  • [MeSH-major] Anus Diseases / etiology. Histiocytosis, Langerhans-Cell / diagnosis

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  • [Copyright] Copyright 2009 Elsevier Masson SAS. All rights reserved.
  • (PMID = 19864102.001).
  • [ISSN] 0399-8320
  • [Journal-full-title] Gastroentérologie clinique et biologique
  • [ISO-abbreviation] Gastroenterol. Clin. Biol.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] France
  • [Chemical-registry-number] 0 / Antineoplastic Agents, Phytogenic; 0 / Glucocorticoids; 5V9KLZ54CY / Vinblastine; VB0R961HZT / Prednisone
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63. Schmidt GP, Reiser MF, Baur-Melnyk A: Whole-body imaging of bone marrow. Semin Musculoskelet Radiol; 2009 Jun;13(2):120-33
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  • For bone marrow screening, multimodality algorithms including conventional radiographs, bone scintigraphy, multislice computed tomography CT (MS-CT) scan, and dedicated magnetic resonance imaging (MRI) are widely established in clinical routine.
  • Therefore, skeletal scintigraphy often is used as a more sensitive and integrated method in patients with suspected malignant bone marrow disease.
  • Hybrid imaging concepts, such as positron emission tomography-computed tomography (PET-CT) scan, have been established as an effective tool for the detection of skeletal metastases, using the additional metabolic information of a PET scan for the assessment of tumor viability and therapy response.
  • WB-MRI has successfully been applied for screening of bone metastases and hematologic bone marrow diseases, like multiple myeloma, lymphoma, and histiocytosis X.
  • [MeSH-minor] Aged. Algorithms. Bone Neoplasms / pathology. Bone Neoplasms / secondary. Child. Histiocytosis, Langerhans-Cell / pathology. Humans. Lymphoma / pathology. Multiple Myeloma / pathology. Positron-Emission Tomography. Young Adult

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  • (PMID = 19455475.001).
  • [ISSN] 1098-898X
  • [Journal-full-title] Seminars in musculoskeletal radiology
  • [ISO-abbreviation] Semin Musculoskelet Radiol
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] United States
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64. Sager S, Yilmaz S, Sager G, Halac M: Tc 99m bone scan and fluorodeoxyglucose positron emission tomography in evaluation of disseminated langerhans cell histiocytosis. Indian J Nucl Med; 2010 Oct;25(4):164-7

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Tc 99m bone scan and fluorodeoxyglucose positron emission tomography in evaluation of disseminated langerhans cell histiocytosis.
  • Langerhans cell histiocytosis (LCH) is a rare histiocytic disorder in which pathological langerhans cells accumulate in a variety of organs.
  • In this case report we present fluorine-18 positron emission tomography (F-18 PET/CT) and bone scintigraphy findings of a 18-year-old male patient with disseminated LCH, mimicking multiple hypermetabolic metastatic lesions.
  • Clinicians should be aware that LCH infiltrations can be seen as intense uptake and to differentiate infiltrations from other metastatic intense uptake with fluorodeoxyglucose PET/CT and bone scintigraphy, clinical and laboratory findings should be kept in mind.

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  • [Cites] Leuk Lymphoma. 2002 Nov;43(11):2155-7 [12533041.001]
  • [Cites] J Orthop Sci. 2003;8(3):435-41 [12768492.001]
  • [Cites] Pediatr Radiol. 2003 Sep;33(9):598-602 [12879314.001]
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  • [Cites] Ann Nucl Med. 2008 Oct;22(8):715-7 [18982475.001]
  • (PMID = 21713226.001).
  • [ISSN] 0974-0244
  • [Journal-full-title] Indian journal of nuclear medicine : IJNM : the official journal of the Society of Nuclear Medicine, India
  • [ISO-abbreviation] Indian J Nucl Med
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] India
  • [Other-IDs] NLM/ PMC3109824
  • [Keywords] NOTNLM ; Bone scan / FDG PET/CT / Tc-99m MDP / langerhans cell histiocytosis
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65. Anabi A, Tarrass F, Hachim K, Aghai R, Benghanem MG, Ramdani B, Zaid D, El Attar H, Badr L, Sqalli S: Nephrotic syndrome revealing a disseminated Langerhans' cell histiocytosis. J Nephrol; 2005 Nov-Dec;18(6):777-80
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Nephrotic syndrome revealing a disseminated Langerhans' cell histiocytosis.
  • Langerhans' cell histiocytosis (LCH) is a clonal disorder of proliferating histiocytes, which can affect various organs.
  • The clinical picture ranges from localized to disseminated disease with multiple organ involvement and severe organ dysfunction.
  • We report here a case of nephrotic syndrome caused by membranoproliferative glomerulonephritis (MPGN) in a 20-year-old woman, which revealed a disseminated form of LCH.
  • Surgical removal of the LCH process and high doses of corticosteroids led to the remission of the basic disease and the renal involvement.
  • The occurence of membranoproliferative glomerulonephritis in the course of LCH might be mediated by circulating immune complexes, composed at least in part of antigens or neoantigenes which may cause the abnormal proliferation of the Langerhans' cells.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / complications. Nephrotic Syndrome / etiology

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  • (PMID = 16358239.001).
  • [ISSN] 1121-8428
  • [Journal-full-title] Journal of nephrology
  • [ISO-abbreviation] J. Nephrol.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Italy
  • [Chemical-registry-number] 0 / Glucocorticoids
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66. Yu G, Huang F, Kong L, Kong X, Zhang L, Xu Q: Langerhans cell histiocytosis of the sphenoid sinus: a case report. Turk J Pediatr; 2010 Sep-Oct;52(5):548-51
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  • [Title] Langerhans cell histiocytosis of the sphenoid sinus: a case report.
  • Langerhans cell histiocytosis (LCH), previously known as histiocytosis X, is a rare disorder characterized by clonal proliferation and excess accumulation of pathologic Langerhans cells causing local or systemic effects.
  • Surgery was performed and the disease was diagnosed pathologically as single-site LCH via hematoxylin-eosin (H&E) and immunohistochemical staining.

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  • (PMID = 21434545.001).
  • [ISSN] 0041-4301
  • [Journal-full-title] The Turkish journal of pediatrics
  • [ISO-abbreviation] Turk. J. Pediatr.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article; Research Support, Non-U.S. Gov't
  • [Publication-country] Turkey
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67. Demaerel P, Van Gool S: Paediatric neuroradiological aspects of Langerhans cell histiocytosis. Neuroradiology; 2008 Jan;50(1):85-92
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Paediatric neuroradiological aspects of Langerhans cell histiocytosis.
  • Langerhans cell histiocytosis, previously known as histiocytosis X, is a complex disease consisting of three entities that are all characterized by a proliferation of the Langerhans cell.
  • The clinical course is variable and ranges from a solitary lytic bone or skin lesion with complete remission to a multisystem disorder with possible lethal outcome.
  • The clinical suspicion can be increased based on radiological findings that are important criteria in defining the extent of the disease involvement.
  • A biopsy is often necessary for establishing the final diagnosis.
  • The lytic craniofacial bone lesions are the most common craniospinal abnormality in Langerhans cell histiocytosis.
  • It is important to be able to recognize the extensive spectrum of neuroradiological abnormalities in order to arrive at the diagnosis.
  • [MeSH-major] Central Nervous System Diseases / diagnosis. Histiocytosis, Langerhans-Cell / diagnosis. Magnetic Resonance Imaging. Tomography, X-Ray Computed
  • [MeSH-minor] Brain / pathology. Child. Choroid Plexus / pathology. Diagnosis, Differential. Follow-Up Studies. Humans. Meninges / pathology. Pituitary Gland / pathology. Skull / pathology. Spine / pathology


68. Ghavamzadeh A, Alimoghaddam K, Jahani M, Mousavi SA, Iravani M, Bahar B, Khodabandeh A, Khatami F, Ghaffari F, Jalali A: Stem cell transplantation; Iranian experience. Arch Iran Med; 2009 Jan;12(1):69-72
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  • [Title] Stem cell transplantation; Iranian experience.
  • From March 1991 through 31st December 2007, 2042 patients underwent stem cell transplantation at the Hematology-Oncology and Stem Cell Transplantation Research Center, affiliated to Tehran University of Medical Sciences.
  • These transplantations included 1405 allogeneic stem cell transplantation, 624 autologous stem cell transplantation, and 13 syngeneic stem cell transplantation.
  • Stem cell transplantation was performed for various diseases including acute myelogenous leukemia, acute lymphoblastic leukemia, chronic myelogenous leukemia, chronic lymphoblastic leukemia, thalassemia major, sickle cell thalassemia, sickle cell disease, multiple myeloma, myelodysplasia, mucopolysaccharidosis, paroxysmal nocturnal hemoglobinuria, non-Hodgkin's lymphoma, Hodgkin's disease, severe aplastic anemia, plasma cell leukemia, Niemann-Pick disease, Fanconi anemia, severe combine immunodeficiency, congenital neutropenia, leukocyte adhesion deficiencies, Chediak-Higashi syndrome, osteopetrosis, histiocytosis X, Hurler syndrome, amyloidosis, systemic sclerosis, breast cancer, Ewing's sarcoma, testicular cancer, germ cell tumors, neuroblastoma, medulloblastoma, renal cell carcinoma, nasopharyngeal carcinoma, ovarian cancer, Wilms' tumor, rhabdomyosarcoma, pancreatoblastoma, and multiple sclerosis.
  • We had 105 cellular therapies for postmyocardial infarction, multiple sclerosis, cirrhosis, head of femur necrosis, and renal cell carcinoma.
  • About 74.9% of the patients (1530 of 2042) remained alive between one to 168 months after stem cell transplantation.
  • Nearly 25.1% (512 of 2042) of our patients died after stem cell transplantation.
  • The causes of deaths were relapse, infections, hemorrhagic cystitis, graft versus host disease, and others.
  • [MeSH-major] Hematologic Neoplasms / surgery. Stem Cell Transplantation / methods

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  • [ErratumIn] Arch Iran Med. 2009 May;12(3):329. Alimogaddam, Kamran [corrected to Alimoghaddam, Kamran]; Mousavi, Seyed Asadollah [corrected to Mousavi, Seied Asadollah]
  • [ErratumIn] Arch Iran Med. 2012 Aug;15(8):524
  • (PMID = 19111033.001).
  • [ISSN] 1029-2977
  • [Journal-full-title] Archives of Iranian medicine
  • [ISO-abbreviation] Arch Iran Med
  • [Language] eng
  • [Publication-type] Comparative Study; Journal Article
  • [Publication-country] Iran
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69. Fuertes Cabero S, Fuster Pelfort D, Setoain Perego X, González Berenguer J, Mateos Fernández JJ, Paredes Barranco P, Ortín Pérez J, Pons Pons F: [Usefulness of bone scintigraphy for staging in a case of histiocytosis of the temporal bone]. Rev Esp Med Nucl; 2005 Jan-Feb;24(1):45-7
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  • [Title] [Usefulness of bone scintigraphy for staging in a case of histiocytosis of the temporal bone].
  • [Transliterated title] La gammagrafía ósea demuestra ser útil para el diagnóstico de extensión en un caso de histiocitosis X del hueso temporal.
  • We present the case of a 43-year-old man diagnosed of insipid diabetes and hypogonadotropic hypogonadism in whom a right temporal bone lesion was observed in the control MRI, thus leading to his admission.
  • A biopsy on the newly appearing mouth ulcers in the jugal mucous was performed and showed Langerhan's cells, the diagnosis of histiocytosis X being confirmed.
  • Six months later a new MRI indicated disease progression with bilateral temporal involvement.
  • The bone scan findings in this case provided a more exact extension diagnosis of the disease than the MRI.
  • [MeSH-major] Bone Diseases / radionuclide imaging. Histiocytosis, Langerhans-Cell / radionuclide imaging. Temporal Bone / radionuclide imaging

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  • (PMID = 15701346.001).
  • [ISSN] 0212-6982
  • [Journal-full-title] Revista española de medicina nuclear
  • [ISO-abbreviation] Rev Esp Med Nucl
  • [Language] spa
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] Spain
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70. Kapur P, Erickson C, Rakheja D, Carder KR, Hoang MP: Congenital self-healing reticulohistiocytosis (Hashimoto-Pritzker disease): ten-year experience at Dallas Children's Medical Center. J Am Acad Dermatol; 2007 Feb;56(2):290-4
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  • [Title] Congenital self-healing reticulohistiocytosis (Hashimoto-Pritzker disease): ten-year experience at Dallas Children's Medical Center.
  • The real incidence of congenital self-healing reticulohistiocytosis (CSHR) may be underreported because of its high rate of spontaneous resolution and lack of clinical recognition.
  • Currently, there are no criteria other than clinical that can reliably distinguish CSHR from cutaneous involvement by disseminated Langerhans cell histiocytosis (LCH).
  • In this study we investigate the role of E-cadherin, Ki-67, and phosphorylated histone H3 (PHH3) immunohistochemical stains in distinguishing CSHR from disseminated LCH.
  • We found that no significant difference was seen in the histologic features and the expression of E-cadherin, Ki-67, and PHH3 between the two groups; thus supporting the theory that CSHR and LCH represent different ends of a spectrum of the same condition.
  • [MeSH-major] Cadherins / metabolism. Histiocytosis, Non-Langerhans-Cell / diagnosis. Histiocytosis, Non-Langerhans-Cell / metabolism. Histones / metabolism. Ki-67 Antigen / metabolism
  • [MeSH-minor] Female. Histiocytosis, Langerhans-Cell / diagnosis. Humans. Immunohistochemistry. Infant. Infant, Newborn. Male. Retrospective Studies

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  • (PMID = 17224372.001).
  • [ISSN] 1097-6787
  • [Journal-full-title] Journal of the American Academy of Dermatology
  • [ISO-abbreviation] J. Am. Acad. Dermatol.
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] United States
  • [Chemical-registry-number] 0 / Cadherins; 0 / Histones; 0 / Ki-67 Antigen
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71. Elas D, Benda JA, Galask RP: Langerhans' cell histiocytosis of the vulva: the Iowa experience. J Reprod Med; 2008 Jun;53(6):417-9
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Langerhans' cell histiocytosis of the vulva: the Iowa experience.
  • BACKGROUND: Vulvar presentation of Langerhans' cell histiocytosis (histiocytosis X) is rare.
  • Symptoms and signs at the time of presentation can include pruritus, pain, dyspareunia, burning, discharge and presence of a discrete lesion and/or generalized ulceration.
  • Once a diagnosis of Langerhans' cell histiocytosis is made, there is no formal treatment protocol.
  • This report highlights 2 clinical cases diagnosed and treated at a tertiary care center.
  • CASES: We report the case histories of 2 women who presented to the Vulva/Vaginal Disease Clinic at the University of Iowa.
  • The second patient, a 39-year-old woman, had a 3-month history of a clitoral growth.
  • CONCLUSION: Presentation of Langerhans' cell histiocytosis as a vulvar primary condition is rare and probably underdiagnosed as its clinical presentation can vary.
  • Langerhans' cell histiocytosis should be considered as a differential diagnosis in females who present with chronic pruritus, pain, ulcerations or intermittent rashes.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / complications. Histiocytosis, Langerhans-Cell / diagnosis. Vulvar Diseases / diagnosis. Vulvar Diseases / etiology

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  • [CommentIn] J Reprod Med. 2009 Jun;54(6):411 [19639935.001]
  • (PMID = 18664059.001).
  • [ISSN] 0024-7758
  • [Journal-full-title] The Journal of reproductive medicine
  • [ISO-abbreviation] J Reprod Med
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] United States
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72. Majchrzak K, Bierzyńska-Macyszyn G, Bobek-Billewicz B, Majchrzak H, Ładziński P: Rare primary tumours of the hypothalamus in adults: clinical course and surgical treatment. Neurol Neurochir Pol; 2010 Nov-Dec;44(6):546-53

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  • [Title] Rare primary tumours of the hypothalamus in adults: clinical course and surgical treatment.
  • There were 2 patients with craniopharyngiomas located exclusively in the third ventricle, and single patients with gemistocytic astrocytoma, Langerhans cell histiocytosis X and hamartoma of the hypothalamus each.

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  • (PMID = 21225516.001).
  • [ISSN] 0028-3843
  • [Journal-full-title] Neurologia i neurochirurgia polska
  • [ISO-abbreviation] Neurol. Neurochir. Pol.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Poland
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73. Brown CW, Jarvis JG, Letts M, Carpenter B: Treatment and outcome of vertebral Langerhans cell histiocytosis at the Children's Hospital of Eastern Ontario. Can J Surg; 2005 Jun;48(3):230-6
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  • [Title] Treatment and outcome of vertebral Langerhans cell histiocytosis at the Children's Hospital of Eastern Ontario.
  • BACKGROUND: We wished to evaluate the treatment methods for vertebral Langerhans cell histiocytosis (LCH) (a rare reticuloendothelial disorder) at a tertiary care pediatric centre and compare treatment and outcomes with those reported in the recent literature.
  • Only those children who were under 18 years of age, had a diagnosis of LCH, histiocytosis X or eosinophilic granuloma and had documented vertebral involvement were included.
  • Treatment depends on the severity of the disease.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / surgery. Spinal Diseases / surgery


74. Hausbrandt PA, Leithner A, Beham A, Bodo K, Raith J, Windhager R: A rare case of infantile myofibromatosis and review of literature. J Pediatr Orthop B; 2010 Jan;19(1):122-6
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  • [Title] A rare case of infantile myofibromatosis and review of literature.
  • Infantile myofibromatosis is a rare benign tumor-disease (1/400,000).
  • We would like to present a rare case of a multicentric type with singular visceral involvement and a literature review of all case series with more than five patients.
  • The rapid frozen section biopsy hinted at the diagnosis of histiocytosis X.
  • The definitive histological result 6 days later was infantile myofibromatosis.
  • Infantile myofibromatosis is a very rare benign tumor-disease.
  • These findings also can be interpreted as histiocytosis X, which is a potential differential diagnosis.
  • In conclusion, the present case report and the literature review support the notion that infantile myofibromatosis should be considered as a possible differential diagnosis for soft tissue expansions and/or osteolytic lesions in a newborn.
  • [MeSH-minor] Calcinosis / pathology. Calcinosis / physiopathology. Diagnosis, Differential. Follow-Up Studies. Frozen Sections. Histiocytosis, Langerhans-Cell / diagnosis. Humans. Infant. Male. Neoplasm Regression, Spontaneous

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  • (PMID = 19738495.001).
  • [ISSN] 1473-5865
  • [Journal-full-title] Journal of pediatric orthopedics. Part B
  • [ISO-abbreviation] J Pediatr Orthop B
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article; Review
  • [Publication-country] United States
  • [Number-of-references] 18
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75. Larralde M, Abad ME, Gomar B: [Langerhans cell histiocytosis in children under one year]. Arch Argent Pediatr; 2008 Jun;106(3):269-72
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Langerhans cell histiocytosis in children under one year].
  • [Transliterated title] Histiocitosis de células de Langerhans en menores de un año.
  • INTRODUCTION: Langerhans cell histiocytosis is characterized by a clonal proliferation of activated Langerhans cells that infiltrate various organs of the body.
  • OBJECTIVE: To describe the morphologyc characteristics of skin lesions and clinical course of 15 patients with Langerhans cell histiocytosis.
  • METHODS: A retrospective review of the medical records of patients with Langerhans cell histiocytosis from Ramos Mejia Hospital and Aleman Hospital, between 1999-2007.
  • The patients with congenital presentation only had a cutaneous manifestation; one patient who developed a systemic compromise (lung, liver and spleen) is currently under treatment.
  • Three patients with presentation after birth only had cutaneous lesions, the others had a systemic disease.
  • CONCLUSION: Both clinical manifestation (congenital and after birth) represent different ends of a spectrum of the same condition, with the potencial to develop into disseminated Langerhans cell histiocytosis.
  • [MeSH-major] Histiocytosis, Langerhans-Cell

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  • (PMID = 18695843.001).
  • [ISSN] 1668-3501
  • [Journal-full-title] Archivos argentinos de pediatría
  • [ISO-abbreviation] Arch Argent Pediatr
  • [Language] spa
  • [Publication-type] English Abstract; Journal Article
  • [Publication-country] Argentina
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76. Steiner QG, Otten LA, Hicks MJ, Kaya G, Grosjean F, Saeuberli E, Lavanchy C, Beermann F, McClain KL, Acha-Orbea H: In vivo transformation of mouse conventional CD8alpha+ dendritic cells leads to progressive multisystem histiocytosis. Blood; 2008 Feb 15;111(4):2073-82
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] In vivo transformation of mouse conventional CD8alpha+ dendritic cells leads to progressive multisystem histiocytosis.
  • Whether abnormal proliferation of dendritic cells causes Langerhans cell histiocytosis (LCH) is a highly debated topic.
  • The transformed cells were differentiated splenic CD8 alpha-positive conventional dendritic cells with increased Langerin expression.
  • Mice developed a DC disease involving the spleen, liver, bone marrow, thymus, and mesenteric lymph node.
  • Surprisingly, lesions displayed key immunohistologic features of Langerhans cell histiocytosis, including expression of Langerin and absence of the abnormal mitoses observed in Langerhans cell sarcomas.
  • Our results demonstrate that a transgenic mouse model with striking similarities to aggressive forms of multisystem histiocytosis, such as the Letterer-Siwe syndrome, can be obtained by transformation of conventional DCs.
  • They can reveal shared molecular pathways for human histiocytosis between humans and mice.
  • [MeSH-major] Antigens, CD8 / immunology. Dendritic Cells / immunology. Histiocytosis, Langerhans-Cell / immunology. Lymphocyte Activation / immunology

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  • (PMID = 18029555.001).
  • [ISSN] 0006-4971
  • [Journal-full-title] Blood
  • [ISO-abbreviation] Blood
  • [Language] eng
  • [Publication-type] Journal Article; Research Support, Non-U.S. Gov't
  • [Publication-country] United States
  • [Chemical-registry-number] 0 / Antigens, CD11c; 0 / Antigens, CD8; 0 / CD8alpha antigen; 0 / DNA Primers; 0 / Genetic Markers; 147336-22-9 / Green Fluorescent Proteins
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77. Mauro E, Fraulini C, Rigolin GM, Galeotti R, Spanedda R, Castoldi G: A case of disseminated Langerhans' cell histiocytosis treated with thalidomide. Eur J Haematol; 2005 Feb;74(2):172-4
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] A case of disseminated Langerhans' cell histiocytosis treated with thalidomide.
  • Tumor necrosis factor alpha (TNF-alpha) seems to play a key role in the pathogenesis of Langerhans' cell histiocytosis (LCH).
  • To our knowledge this is the first case of disseminated LCH successfully treated with thalidomide.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / drug therapy. Immunosuppressive Agents / administration & dosage. Thalidomide / administration & dosage
  • [MeSH-minor] Aged. Female. Humans. Langerhans Cells / metabolism. Langerhans Cells / pathology. Tomography, X-Ray Computed. Tumor Necrosis Factor-alpha / metabolism

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  • [Copyright] (c) Blackwell Munksgaard 2005
  • (PMID = 15654911.001).
  • [ISSN] 0902-4441
  • [Journal-full-title] European journal of haematology
  • [ISO-abbreviation] Eur. J. Haematol.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article; Research Support, Non-U.S. Gov't
  • [Publication-country] Denmark
  • [Chemical-registry-number] 0 / Immunosuppressive Agents; 0 / Tumor Necrosis Factor-alpha; 4Z8R6ORS6L / Thalidomide
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78. Chen W, Wang J, Wang E, Lu Y, Lau SK, Weiss LM, Huang Q: Detection of clonal lymphoid receptor gene rearrangements in langerhans cell histiocytosis. Am J Surg Pathol; 2010 Jul;34(7):1049-57
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Detection of clonal lymphoid receptor gene rearrangements in langerhans cell histiocytosis.
  • Langerhans cell histiocytosis (LCH), also known as histiocytosis X, is a rare human disorder characterized by an abnormal accumulation and/or clonal proliferation of Langerhans cells (LCs) in various body organs.
  • In human LCH, concomitant or sequential occurrence of a lymphoid or myeloid malignancy has been occasionally reported, suggesting the presence of lineage plasticity and/or the possibility of transdifferentiation of 2 otherwise morphologically and immunophenotypically different neoplasms.
  • To gain a better understanding of the pathogenesis and cellular origin of human LCH, we retrospectively investigated 46 well-characterized LCH cases to detect clonal rearrangements of T-cell receptor gamma gene (TRG@) and immunoglobulin heavy chain and kappa light chain genes (IGH@/IGK@).
  • None (0/46) of the cases had a known history or concurrent B or T-cell lymphoma.
  • Interestingly, of the 14 cases with at least one clonal rearrangement of lymphoid receptor genes, 3 LCH cases were shown to have both TRG@ and IGH@/IGK@ gene rearrangements, but failed to express T-cell or B-cell lineage specific or associated markers, suggesting lineage plasticity or infidelity of the neoplasm.
  • [MeSH-major] Gene Rearrangement, B-Lymphocyte. Gene Rearrangement, beta-Chain T-Cell Antigen Receptor. Histiocytosis, Langerhans-Cell / pathology. Langerhans Cells / pathology
  • [MeSH-minor] Adolescent. Adult. Cell Lineage. Child. Child, Preschool. Clone Cells. DNA, Neoplasm / analysis. Female. Humans. Immunoglobulin Heavy Chains / genetics. Immunoglobulin kappa-Chains / genetics. Immunohistochemistry. Immunophenotyping. Infant. Male. Middle Aged. Receptors, Antigen, T-Cell, gamma-delta / genetics. Retrospective Studies. Young Adult

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  • (PMID = 20551822.001).
  • [ISSN] 1532-0979
  • [Journal-full-title] The American journal of surgical pathology
  • [ISO-abbreviation] Am. J. Surg. Pathol.
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] United States
  • [Chemical-registry-number] 0 / DNA, Neoplasm; 0 / Immunoglobulin Heavy Chains; 0 / Immunoglobulin kappa-Chains; 0 / Receptors, Antigen, T-Cell, gamma-delta
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79. López-Meseguer M, Román A, Monforte V, Bravo C, Solé J, Morell F: [Double-lung transplantation in 15 patients with pulmonary hypertension]. Arch Bronconeumol; 2009 Aug;45(8):366-70
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Transliterated title] Trasplante bipulmonar en hipertensión pulmonar. Una serie de 15 pacientes.
  • BACKGROUND: Pulmonary hypertension is a serious disease that, in its terminal phase, requires lung transplantation.
  • Clinical data recorded before the procedure and during follow-up were reviewed.
  • The remaining causes were documented as chronic peripheral pulmonary embolism, histiocytosis X, venoocclusive disease, scleroderma, and simple corrected congenital heart defect in 1 patient each.
  • The mean time between diagnosis of pulmonary hypertension and lung transplantation was 5.9 years (range, 0.4-20 y).
  • [MeSH-minor] Adult. Brassica. Bronchiolitis Obliterans / etiology. Bronchiolitis Obliterans / mortality. CREST Syndrome / complications. Cardiovascular Diseases / complications. Combined Modality Therapy. Epoprostenol / therapeutic use. Female. Follow-Up Studies. Graft Rejection. Hemodynamics. Histiocytosis, Langerhans-Cell / complications. Humans. Infection / etiology. Infection / mortality. Male. Middle Aged. Plant Oils / poisoning. Postoperative Complications / epidemiology. Retrospective Studies. Survival Analysis. Treatment Outcome. Young Adult


80. Rahman H, Yeh S, Albini TA, Carvounis P, Paysse EA, Holz ER: Chorioretinitis and panuveitis in an infant with systemic langerhans cell histiocytosis. Retin Cases Brief Rep; 2009;3(2):204-6

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Chorioretinitis and panuveitis in an infant with systemic langerhans cell histiocytosis.
  • BACKGROUND: Panuveitis and chorioretinitis in infants with Langerhans cell histiocytosis are rare and fundus photographic documentation is lacking in the literature.
  • RESULTS: The authors report a case of an infant with disseminated Langerhans cell histiocytosis who presented with panuveitis in the right eye and chorioretinitis in left eye.
  • CONCLUSION: The authors recommend examination of infants with Langerhans cell histiocytosis for chorioretinal involvement.

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  • (PMID = 25391076.001).
  • [ISSN] 1935-1089
  • [Journal-full-title] Retinal cases & brief reports
  • [ISO-abbreviation] Retin Cases Brief Rep
  • [Language] eng
  • [Publication-type] Journal Article
  • [Publication-country] United States
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81. Palazzini M, Manes A, Negro L, Marinelli A, Leci E, Gambetti S, Bachetti C, Beciani E, Conficoni E, Branzi A, Galiè N: [Pulmonary arterial hypertension. Part I: pathobiologic, pathophysiologic, clinical and diagnostic aspects]. G Ital Cardiol (Rome); 2009 May;10(5):271-300
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Pulmonary arterial hypertension. Part I: pathobiologic, pathophysiologic, clinical and diagnostic aspects].
  • Pulmonary hypertension is present in multiple clinical conditions which have been classified in five groups.
  • Pulmonary arterial hypertension (group 1) includes the familial and the idiopathic form and the forms associated with anorexigen drug use, connective tissue diseases, congenital heart diseases, HIV infection and portal hypertension.
  • Group 3 includes parenchymal lung diseases (chronic obstructive lung disease, lung fibrosis, ecc).
  • Group 5 includes heterogeneous conditions such as sarcoidosis and histiocytosis X.
  • These clinical groups are characterized by different pathobiologic and pathophysiologic mechanisms and therapeutic strategies.
  • Genetic factors (inheritable forms), predisposing factors (female gender) and exogenous factors (drugs, antibodies, viruses, congenital heart disease, etc).
  • Current approved therapies are targeted to the correction of this imbalance, which leads to the progressive increase of pulmonary vascular resistance.
  • [MeSH-major] Hypertension, Pulmonary / diagnosis. Hypertension, Pulmonary / physiopathology


82. Chaudhary A, Debnath J, Thulkar S, Seth T, Sinha A: Imaging findings in hepatic Langerhans' cell histiocytosis. Indian J Pediatr; 2006 Nov;73(11):1036-8
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Imaging findings in hepatic Langerhans' cell histiocytosis.
  • We describe ultrasonographic and computed tomographic features of hepatic lesions in two cases of disseminated Langerhans' cell histiocytosis affecting children.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / radiography. Histiocytosis, Langerhans-Cell / ultrasonography. Liver Diseases / radiography. Liver Diseases / ultrasonography

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  • (PMID = 17127788.001).
  • [ISSN] 0973-7693
  • [Journal-full-title] Indian journal of pediatrics
  • [ISO-abbreviation] Indian J Pediatr
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] India
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83. Trotz M, Weber MA, Jacques TS, Malone M, Sebire NJ: Disseminated langerhans cell histiocytosis-related sudden unexpected death in infancy. Fetal Pediatr Pathol; 2009;28(1):39-44
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Disseminated langerhans cell histiocytosis-related sudden unexpected death in infancy.
  • Sudden unexpected death in infancy (SUDI) is defined as the sudden and unexpected death of an infant aged less than 1 year and comprises a heterogeneous group of deaths; in around one-third of cases a definite cause of death is identified at autopsy, while almost two-thirds of such deaths will remain unexplained despite a careful review of the circumstances of death and a detailed postmortem examination.
  • We report a case of SUDI due to previously undiagnosed disseminated Langerhans cell histiocytosis (LCH) in a 10-month-old male, a disease characterized by a clonal proliferation of dendritic Langerhans cells.
  • The diagnosis was established on histological examination, which revealed extensive infiltration by LCH of the skin, lymph nodes, thymus, spleen, and lungs.
  • Despite a high mortality in disseminated disease, to our knowledge, this is the first reported case in the English-language literature of disseminated multisystem Langerhans cell disease presenting as SUDI.
  • Furthermore, this case demonstrates the importance of routine microscopic tissue sampling in all SUDI, as the diagnosis required histological examination of the organs and might have been missed had histology not been performed.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / complications. Histiocytosis, Langerhans-Cell / pathology. Sudden Infant Death / etiology


84. Nguyen BD, Roarke MC, Chivers SF: Multifocal Langerhans cell histiocytosis with infiltrative pelvic lesions: PET/CT imaging. Clin Nucl Med; 2010 Oct;35(10):824-6
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  • [Title] Multifocal Langerhans cell histiocytosis with infiltrative pelvic lesions: PET/CT imaging.
  • Langerhans cell histiocytosis is essentially a pediatric disorder with a large spectrum encompassing focal lytic osseous eosinophilic granuloma, chronic multifocal Hand-Schuller-Christian lesions, and fulminant disseminated Letterer-Siwe syndrome.
  • The authors present a case of multifocal Langerhans cell histiocytosis in a 47-year-old woman.
  • The PET/CT-depicted infiltrative features of soft tissue and osseous pelvic lesions with obstructive uropathy are unusual for this disease.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / radiography. Histiocytosis, Langerhans-Cell / radionuclide imaging. Pelvis / pathology. Positron-Emission Tomography. Tomography, X-Ray Computed

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  • (PMID = 20838300.001).
  • [ISSN] 1536-0229
  • [Journal-full-title] Clinical nuclear medicine
  • [ISO-abbreviation] Clin Nucl Med
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] United States
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85. Ivanov A, Mihăilă D, Miron I, Plămădeală P, Tansanu I: [Children's Langerhans cell histiocytosis, diagnostic problems]. Rev Med Chir Soc Med Nat Iasi; 2010 Apr-Jun;114(2):424-7
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Children's Langerhans cell histiocytosis, diagnostic problems].
  • [Transliterated title] Probleme de diagnostic în histiocitoza langerhans la copil.
  • Langerhans cell histiocytosis is a group of idiopathic disorders characterized by the proliferation of cells of the mononuclear phagocyte system and the dendritic cell system.
  • From the clinical point of view there are 3 forms of histiocytosis encountered in child pathology: acute, disseminated called Abt-Letterer-Siwe (it usually affects children under 2 years of age), eosinophilic granuloma and the intermediate clinical form called Hand-Schuller-Christian disease.
  • We present the case of a premature born child that had, even from the day she was born, a rash disseminated on the entire surface of the body associated with enlarged lymph nodes, hepatosplenomegaly and thrombocytopenia.
  • The diagnosis of Langerhans cell Histiocytosis is difficult to establish and this case is an example that confirms it.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / diagnosis
  • [MeSH-minor] Diagnosis, Differential. Exanthema / etiology. Fatal Outcome. Female. Hepatomegaly / etiology. Humans. Infant, Newborn. Infant, Premature. Lymphatic Diseases / etiology. Risk Factors. Splenomegaly / etiology

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  • (PMID = 20700979.001).
  • [ISSN] 0048-7848
  • [Journal-full-title] Revista medico-chirurgicală̆ a Societă̆ţ̜ii de Medici ş̧i Naturaliş̧ti din Iaş̧i
  • [ISO-abbreviation] Rev Med Chir Soc Med Nat Iasi
  • [Language] rum
  • [Publication-type] Case Reports; English Abstract; Journal Article
  • [Publication-country] Romania
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86. Natsume H, Yamaguchi T, Ohsawa J, Hongoh T, Ohzeki T, Kojima K, Yasuda S, Shamoto M: Splenic infarction in Letterer-Siwe disease. Pediatr Int; 2005 Jun;47(3):329-32

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Splenic infarction in Letterer-Siwe disease.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / pathology. Splenic Infarction / pathology

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  • (PMID = 15910461.001).
  • [ISSN] 1328-8067
  • [Journal-full-title] Pediatrics international : official journal of the Japan Pediatric Society
  • [ISO-abbreviation] Pediatr Int
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Australia
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87. Mohammed A, Yau LZ, Samaila MO, Ahmed SA, Chom ND: Histiocytosis X. Ann Afr Med; 2009 Jan-Mar;8(1):64-5
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Histiocytosis X.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / pathology

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  • (PMID = 19763012.001).
  • [ISSN] 0975-5764
  • [Journal-full-title] Annals of African medicine
  • [ISO-abbreviation] Ann Afr Med
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Nigeria
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88. Fesenko OV, Shappo NV, Duganov VK, Shepelenko AF: [Two cases of histiocytosis X of the lungs]. Ter Arkh; 2007;79(10):77-9
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Two cases of histiocytosis X of the lungs].
  • [MeSH-major] Histiocytosis, Langerhans-Cell / diagnosis
  • [MeSH-minor] Adult. Diagnosis, Differential. Humans. Male. Smoking / adverse effects. Tuberculosis, Pulmonary / diagnosis. Tuberculosis, Pulmonary / drug therapy

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  • (PMID = 18154151.001).
  • [ISSN] 0040-3660
  • [Journal-full-title] Terapevticheskiĭ arkhiv
  • [ISO-abbreviation] Ter. Arkh.
  • [Language] rus
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Russia (Federation)
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89. Fesenko OV: [Pulmonary histiocytosis X]. Ter Arkh; 2007;79(3):70-6
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Pulmonary histiocytosis X].
  • [MeSH-major] Histiocytosis, Langerhans-Cell. Lung / pathology

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  • (PMID = 17526202.001).
  • [ISSN] 0040-3660
  • [Journal-full-title] Terapevticheskiĭ arkhiv
  • [ISO-abbreviation] Ter. Arkh.
  • [Language] rus
  • [Publication-type] Journal Article; Review
  • [Publication-country] Russia (Federation)
  • [Chemical-registry-number] 0 / Adrenal Cortex Hormones
  • [Number-of-references] 87
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90. Materne C, Porubsky S, Gerth J, Gröne HJ, Wolf G: Histiocytosis X and renal insufficiency. Nephrol Dial Transplant; 2007 Dec;22(12):3664-7
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Histiocytosis X and renal insufficiency.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / complications. Renal Insufficiency / etiology

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  • (PMID = 17890248.001).
  • [ISSN] 0931-0509
  • [Journal-full-title] Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association
  • [ISO-abbreviation] Nephrol. Dial. Transplant.
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] England
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91. Hernández Cairo A, Casacó Santana C, Batista Cuéllar JF, Prats Capote A, Coca Pérez MA, Pérez Valdés M: [Image of sepsis associated with histiocytosis X]. Rev Esp Med Nucl; 2008 May-Jun;27(3):205-6
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Image of sepsis associated with histiocytosis X].
  • [Transliterated title] Imagen de sepsis asociada a una histiocitosis X.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / complications. Osteitis / radionuclide imaging. Osteolysis / radionuclide imaging. Staphylococcal Infections / radionuclide imaging. Zygoma / radionuclide imaging

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  • (PMID = 18570865.001).
  • [ISSN] 0212-6982
  • [Journal-full-title] Revista española de medicina nuclear
  • [ISO-abbreviation] Rev Esp Med Nucl
  • [Language] spa
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Spain
  • [Chemical-registry-number] 0 / Organotechnetium Compounds; 0 / Peptide Fragments; 0 / Radiopharmaceuticals; 0 / Ribosomal Proteins; 0 / ribosomal protein S30; 0 / technetium 99m ubiquicidin(29-41)
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92. de Brito Macedo Ferreira LM, de Carvalho JD, Pereira ST, Tavares MG: Histiocytosis X of the temporal bone. Braz J Otorhinolaryngol; 2006 Jul-Aug;72(4):575
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  • [Title] Histiocytosis X of the temporal bone.
  • [MeSH-major] Bone Diseases / diagnosis. Histiocytosis, Langerhans-Cell / diagnosis. Temporal Bone

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  • (PMID = 17143443.001).
  • [ISSN] 1808-8694
  • [Journal-full-title] Brazilian journal of otorhinolaryngology
  • [ISO-abbreviation] Braz J Otorhinolaryngol
  • [Language] eng
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Brazil
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93. Kiakouama L, Cottin V, Etienne-Mastroïanni B, Khouatra C, Humbert M, Cordier JF: Severe pulmonary hypertension in histiocytosis X: long-term improvement with bosentan. Eur Respir J; 2010 Jul;36(1):202-4
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Severe pulmonary hypertension in histiocytosis X: long-term improvement with bosentan.
  • [MeSH-major] Antihypertensive Agents / therapeutic use. Histiocytosis, Langerhans-Cell / drug therapy. Hypertension, Pulmonary / drug therapy. Sulfonamides / therapeutic use


94. Morrison J, Stamenkovic S, Walker WS, Wallace WA: Pulmonary histiocytosis X in a patient with epithelioid mesothelioma. Histopathology; 2006 Sep;49(3):320-1
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  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Pulmonary histiocytosis X in a patient with epithelioid mesothelioma.
  • [MeSH-major] Histiocytosis, Langerhans-Cell / complications. Mesothelioma / complications. Pleural Neoplasms / complications

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  • (PMID = 16918985.001).
  • [ISSN] 0309-0167
  • [Journal-full-title] Histopathology
  • [ISO-abbreviation] Histopathology
  • [Language] eng
  • [Publication-type] Case Reports; Letter
  • [Publication-country] England
  • [Chemical-registry-number] 1332-21-4 / Asbestos
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95. Belhassen-García M, Pardo-Lledías J, Carpio-Pérez A, Velasco-Tirado V, Fuentes-Pardo L, Martín-Barba S, Ruano-Pérez R: [Resolution of a bone lesion in a patient with pulmonary histiocytosis X]. Rev Esp Med Nucl; 2008 Jul-Aug;27(4):277-8
MedlinePlus Health Information. consumer health - Bone Diseases.

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] [Resolution of a bone lesion in a patient with pulmonary histiocytosis X].
  • [Transliterated title] Resolución de lesión ósea en paciente con histiocitosis X pulmonar.
  • [MeSH-major] Bone Diseases / etiology. Bone Diseases / radionuclide imaging. Histiocytosis, Langerhans-Cell / complications. Ribs

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  • (PMID = 18682155.001).
  • [ISSN] 0212-6982
  • [Journal-full-title] Revista española de medicina nuclear
  • [ISO-abbreviation] Rev Esp Med Nucl
  • [Language] spa
  • [Publication-type] Case Reports; Journal Article
  • [Publication-country] Spain
  • [Chemical-registry-number] 0 / Radiopharmaceuticals; 72945-61-0 / technetium Tc 99m hydroxymethylene diphosphonate; X89XV46R07 / Technetium Tc 99m Medronate
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96. Chen RL, Wu PL, Hsu YH, Kuo PL: Evans syndrome after unrelated cord blood transplantation for disseminated Langerhans cell histiocytosis in a child. J Pediatr Hematol Oncol; 2007 May;29(5):348-50
Genetic Alliance. consumer health - Transplantation.

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Evans syndrome after unrelated cord blood transplantation for disseminated Langerhans cell histiocytosis in a child.
  • [MeSH-major] Anemia, Hemolytic, Autoimmune / therapy. Cord Blood Stem Cell Transplantation / methods. Histiocytosis, Langerhans-Cell / therapy. Purpura, Thrombocytopenic, Idiopathic / therapy
  • [MeSH-minor] Antineoplastic Combined Chemotherapy Protocols / administration & dosage. Combined Modality Therapy. Dose-Response Relationship, Drug. Graft vs Host Disease / diagnosis. Graft vs Host Disease / therapy. Humans. Infant. Male. Syndrome. Transplantation, Homologous. Treatment Outcome


97. Corvinus C, Bärtsch P, Dehnert C, Herth FJ, Grünig E: Pulmonary hypertension in a patient with Abt-Letterer-Siwe syndrome and episodes of HAPE. Eur Respir J; 2010 Nov;36(5):1212-4
MedlinePlus Health Information. consumer health - Pulmonary Hypertension.

  • [Source] The source of this record is MEDLINE®, a database of the U.S. National Library of Medicine.
  • [Title] Pulmonary hypertension in a patient with Abt-Letterer-Siwe syndrome and episodes of HAPE.
  • [MeSH-major] Altitude Sickness / complications. Histiocytosis, Langerhans-Cell / complications. Hypertension, Pulmonary / complications. Pulmonary Edema / complications

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  • (PMID = 21037372.001).
  • [ISSN] 1399-3003
  • [Journal-full-title] The European respiratory journal
  • [ISO-abbreviation] Eur. Respir. J.
  • [Language] eng
  • [Publication-type] Case Reports; Letter
  • [Publication-country] Switzerland
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